Clinical trial • Phase III • Neurology|Rare Disease

PRIDOPIDINE HYDROCHLORIDE for Amyotrophic lateral sclerosis

Phase III trial of PRIDOPIDINE HYDROCHLORIDE for Amyotrophic lateral sclerosis.

Overview

Trial Therapeutic Area
Neurology|Rare Disease
Trial Disease
Amyotrophic lateral sclerosis
Trial Stage
Phase III
Drug Modality
Small molecule
Orphan Drug
Yes

Key dates

Initial CTIS Submission Date
18-12-2025
First CTIS Authorization Date
20-04-2026

Trial design

Randomised, pridopidine placebo (pridopidine placebo) — matching placebo control; dose/schedule for placebo not applicable / not specified in the record. Phase III trial in Belgium, France, Germany and others.

Randomised
Yes
Comparator
Pridopidine placebo (Pridopidine placebo) — matching placebo control; dose/schedule for placebo not applicable / not specified in the record.
Target Sample Size
420
Trial Duration For Participant
672

Eligibility

Recruits 420 isVulnerablePopulationSelected = true. Participants are adults aged 18–80. Exclusion criterion: "Presence of unstable psychiatric disease, cognitive impairment, dementia or substance abuse that would impair ability of the participant to provide informed consent and participate in the study" (i.e. participants unable to provide informed consent are excluded). Subject information sheets and informed consent forms (L1 SIS and ICF) are provided (multiple language versions available)..

Vulnerable Population
isVulnerablePopulationSelected = true. Participants are adults aged 18–80. Exclusion criterion: "Presence of unstable psychiatric disease, cognitive impairment, dementia or substance abuse that would impair ability of the participant to provide informed consent and participate in the study" (i.e. participants unable to provide informed consent are excluded). Subject information sheets and informed consent forms (L1 SIS and ICF) are provided (multiple language versions available).

Inclusion criteria

  • {"criterion_text":"- Age 18 to 80 years (both inclusive), at the time of signing the informed consent"}
  • {"criterion_text":"- Definite ALS or Probable ALS using the El Escorial criteria"}
  • {"criterion_text":"- Symptom onset of ≤18 months at screening"}
  • {"criterion_text":"- SVC greater or equal to 60% predicted"}
  • {"criterion_text":"- Treatment Research Initiative to Cure ALS (TRICALS) Risk Profile Calculator score, based on the European Network for the Cure of ALS (ENCALS) survival prediction model in the range of -6 to -2, inclusive, at screening"}

Exclusion criteria

  • {"criterion_text":"- Presence of tracheostomy or permanent assisted ventilation"}
  • {"criterion_text":"- Clinically significant heart disease, clinically significant history of arrhythmia, symptomatic or uncontrolled atrial fibrillation despite treatment, or asymptomatic sustained ventricular tachycardia, or presence of left bundle branch block"}
  • {"criterion_text":"- Presence of unstable psychiatric disease, cognitive impairment, dementia or substance abuse that would impair ability of the participant to provide informed consent and participate in the study"}
  • {"criterion_text":"- Clinically significant and/or unstable medical condition (other than ALS) that may either pose a clinically meaningful risk to the participant and/or to study completion"}
  • {"criterion_text":"- Clinically significant and/or unstable medical condition (other than ALS) that may either pose a clinically meaningful risk to the participant and/or to study completion"}

Endpoints

Primary endpoints

  • {"endpoint_text":"- Change from baseline through Week 26 in the ALSFRS-R total score adjusted for mortality.","definition_or_measurement_approach":"ALSFRS-R total score assessed at baseline and Week 26; analysis adjusted for mortality."}
  • {"endpoint_text":"- Change from baseline through Week 48 in the ALSFRS-R total score adjusted for mortality.","definition_or_measurement_approach":"ALSFRS-R total score assessed at baseline and Week 48; analysis adjusted for mortality."}

Secondary endpoints

  • {"endpoint_text":"- Overall survival at Week 96","definition_or_measurement_approach":"Overall survival assessed through Week 96 (time-to-event/survival outcome)."}
  • {"endpoint_text":"- Change from baseline through Week 26, Week 48 in Speaking rate as measured by quantitative speech assessment in the clinic. Change from baseline through Week 48 in Intelligibility of speech as measured by quantitative speech assessment in the clinic.","definition_or_measurement_approach":"Quantitative speech assessments in clinic measuring speaking rate (Weeks 26 and 48) and intelligibility (through Week 48)."}
  • {"endpoint_text":"- Change from baseline through Week 48 in percent predicted slow vital capacity","definition_or_measurement_approach":"Percent predicted slow vital capacity measured at baseline and Week 48."}
  • {"endpoint_text":"- Change from baseline through Week 48 in the Bulbar subdomain of the ALSFRS-R","definition_or_measurement_approach":"Bulbar subdomain score of ALSFRS-R assessed at baseline and Week 48."}
  • {"endpoint_text":"- Change from baseline through Week 48 in the ALSAQ-40","definition_or_measurement_approach":"ALSAQ-40 quality of life questionnaire score assessed at baseline and Week 48."}
  • {"endpoint_text":"- Incidence, nature, and severity of treatment emergent adverse events, adverse events of special interest, and serious adverse events. Incidence and shifts of clinically significant abnormalities in ECG, laboratory tests, and vital signs. Change from baseline in C-SSRS. Tolerability.","definition_or_measurement_approach":"Safety assessments including AE reporting, ECG/laboratory/vital sign monitoring, C-SSRS suicidality scale changes, and tolerability measures."}

Recruitment

Registry Or Advocacy Recruitment
True, TRICALS Foundation Stichting (Treatment Research Initiative to Cure ALS / TRICALS) is named as providing patient recruitment and site training services
Digital Remote Recruitment
True — planned use of social media posts, online advertisements (banner ads), website content and online study materials to recruit participants; documents include social media/online advertisement materials and website content.
Planned Sample Size
420
Recruitment Window Months
34
Consent Approach
Informed consent is provided by the adult participant (eligible age 18–80). Subject information sheets and informed consent forms (L1_SIS and ICF) are available (multiple language versions listed, e.g. English, French, Dutch, Spanish, Polish). Pregnancy-specific ICFs / partner ICFs are present in documentation. Participants with cognitive impairment or other conditions that impair capacity to consent are excluded per criteria.

Methods

  • Social media and online advertisements (documents: Social Media and Clinical Trial Posts; Online Advertisement Banners) — general public/patients
  • Website content / UMCU website text concept — online information for potential participants
  • Banner ads (online) — outreach to potential participants
  • Patient brochures and participant study guides (patient-facing materials) — information for prospective participants
  • Physician referral letters / physician referral materials — targeting clinicians to refer eligible patients
  • Study brochures and 'About Clinical Trials' brochures — informational outreach to patients and clinicians
  • Direct patient recruitment activities performed by TRICALS Foundation (patient recruitment and site training services)

Geography

Total Number Of Sites
31
Total Number Of Participants
420

Belgium

Earliest CTIS Part Ii Submission Date
27-03-2026
Latest Decision Or Authorization Date
27-04-2026
Processing Time Days
31
Number Of Sites
1
Number Of Participants
25

Sites

Site Name
UZ Leuven
Department Name
Neurology
Principal Investigator Name
Philip Van Damme
Principal Investigator Email
Philip.vandamme@uzleuven.be
Contact Person Name
Philip Van Damme
Contact Person Email
Philip.vandamme@uzleuven.be

France

Earliest CTIS Part Ii Submission Date
16-04-2026
Latest Decision Or Authorization Date
24-04-2026
Processing Time Days
8
Number Of Sites
5
Number Of Participants
60

Sites

Site Name
Assistance Publique Hopitaux De Paris
Department Name
Neurologie
Principal Investigator Name
Gaelle BRUNETEAU
Principal Investigator Email
gaelle.bruneteau@aphp.fr
Contact Person Name
Gaelle BRUNETEAU
Contact Person Email
gaelle.bruneteau@aphp.fr
Site Name
Centre Hospitalier Universitaire De Lille
Department Name
Neurologie
Principal Investigator Name
Veronique DANEL-BRUNAUD
Principal Investigator Email
veronique.danel@chu-lille.fr
Contact Person Name
Veronique DANEL-BRUNAUD
Contact Person Email
veronique.danel@chu-lille.fr
Site Name
Centre Hospitalier Regional De Marseille
Department Name
Centre de Reference des Maladies Neuromusculaires rares et de la Sclérose Latérale Amyotrophique
Principal Investigator Name
Shahram ATTARIAN
Principal Investigator Email
shahram.attarian@ap-hm.fr
Contact Person Name
Shahram ATTARIAN
Contact Person Email
shahram.attarian@ap-hm.fr
Site Name
Centre Hospitalier Universitaire De Nice
Department Name
Neurologie
Principal Investigator Name
Marie-Hélène SORIANI
Principal Investigator Email
soriani.mh@chu-nice.fr
Contact Person Name
Marie-Hélène SORIANI
Contact Person Email
soriani.mh@chu-nice.fr
Site Name
Centre Hospitalier Regional Universitaire De Tours
Department Name
Neurologie
Principal Investigator Name
Philippe CORCIA
Principal Investigator Email
philippe.corcia@univ-tours.fr
Contact Person Name
Philippe CORCIA
Contact Person Email
philippe.corcia@univ-tours.fr

Germany

Earliest CTIS Part Ii Submission Date
13-04-2026
Latest Decision Or Authorization Date
23-04-2026
Processing Time Days
10
Number Of Sites
6
Number Of Participants
72

Sites

Site Name
Charite Universitaetsmedizin Berlin KöR
Department Name
Centrum für Neurologie, Neurochirurgie und Psychiatrie
Principal Investigator Name
Andre Maier
Principal Investigator Email
andre.maier@charite.de
Contact Person Name
Andre Maier
Contact Person Email
andre.maier@charite.de
Site Name
DIAKOVERE Krankenhaus gGmbH
Department Name
Klinik für Neurologie und Neurophysiologie
Principal Investigator Name
Susanne Petri
Principal Investigator Email
susanne.petri@diakovere.de
Contact Person Name
Susanne Petri
Contact Person Email
susanne.petri@diakovere.de
Site Name
Universitaetsklinikum Bonn AöR
Department Name
Klinik für Neurodegenerative Erkrankungen, Motoneuronambulanz
Principal Investigator Name
Patrick Weydt
Principal Investigator Email
patrick.weydt@ukbonn.de
Contact Person Name
Patrick Weydt
Contact Person Email
patrick.weydt@ukbonn.de
Site Name
Universitaetsklinikum Ulm AöR
Department Name
Klinik für Neurologie
Principal Investigator Name
Jochen Weishaupt
Principal Investigator Email
jochen.weishaupt@rku.de
Contact Person Name
Jochen Weishaupt
Contact Person Email
jochen.weishaupt@rku.de
Site Name
Universitaetsklinikum Schleswig-Holstein AöR
Department Name
Klinik für Neurologie, Neuromuskuläres Zentrum Schleswig-Holstein
Principal Investigator Name
Julian Großkreutz
Principal Investigator Email
julian.grosskreutz@uni-luebeck.de
Contact Person Name
Julian Großkreutz
Site Name
Universitaetsklinikum Jena KöR
Department Name
Klinik für Neurologie
Principal Investigator Name
Annekathrin Rödiger
Principal Investigator Email
annekathrin.roediger@med.uni-jena.de
Contact Person Name
Annekathrin Rödiger

Ireland

Earliest CTIS Part Ii Submission Date
02-04-2026
Latest Decision Or Authorization Date
24-04-2026
Processing Time Days
22
Number Of Sites
1
Number Of Participants
25

Sites

Site Name
Beaumont Hospital
Department Name
Neurology
Principal Investigator Name
Orla Hardiman
Principal Investigator Email
HARDIMAO@tcd.ie
Contact Person Name
Orla Hardiman
Contact Person Email
HARDIMAO@tcd.ie

Italy

Earliest CTIS Part Ii Submission Date
13-04-2026
Latest Decision Or Authorization Date
20-04-2026
Processing Time Days
7
Number Of Sites
6
Number Of Participants
72

Sites

Site Name
Azienda Ospedaliera di Padova
Department Name
Centro Regionale Malattie del Motoneurone, UOC Clinica Neurologica Padova
Principal Investigator Name
Gianni Sorarù
Principal Investigator Email
gianni.soraru@unipd.it
Contact Person Name
Gianni Sorarù
Contact Person Email
gianni.soraru@unipd.it
Site Name
Azienda Ospedaliera Universitaria Citta Della Salute E Della Scienza Di Torino
Department Name
SC Neurologia 1 U
Principal Investigator Name
Adriano Chiò
Principal Investigator Email
adriano.chio@unito.it
Contact Person Name
Adriano Chiò
Contact Person Email
adriano.chio@unito.it
Site Name
Azienda Ospedaliero Universitaria Di Modena
Department Name
Ospedale Civile di Baggiovara, Struttura Complessa di Neurologia
Principal Investigator Name
Jessica Mandrioli
Principal Investigator Email
jessica.mandrioli@unimore.it
Contact Person Name
Jessica Mandrioli
Contact Person Email
jessica.mandrioli@unimore.it
Site Name
Centro Clinico Nemo
Department Name
Centro Clinico NeMO di Milano
Principal Investigator Name
Federica Cerri
Principal Investigator Email
federica.cerri@centrocliniconemo.it
Contact Person Name
Federica Cerri
Site Name
Istituto Auxologico Italiano
Department Name
Ospedale San Luca, Neurology Unit
Principal Investigator Name
Nicola Ticozzi
Principal Investigator Email
n.ticozzi@auxologico.it
Contact Person Name
Nicola Ticozzi
Contact Person Email
n.ticozzi@auxologico.it
Site Name
Azienda Ospedaliera Universitaria Universita' Degli Studi Della Campania Luigi Vanvitelli
Department Name
Dipartimento Assistenziale di Medicina Interna, Geriatria e Neurologia
Principal Investigator Name
Francesca Trojsi
Principal Investigator Email
francesca.trojsi@unicampania.it
Contact Person Name
Francesca Trojsi

Spain

Earliest CTIS Part Ii Submission Date
08-04-2026
Latest Decision Or Authorization Date
22-04-2026
Processing Time Days
14
Number Of Sites
6
Number Of Participants
60

Sites

Site Name
Bellvitge University Hospital
Department Name
Neurology
Principal Investigator Name
Monica Povedano Panades
Principal Investigator Email
mpovedano@bellvitgehospital.cat
Contact Person Name
Monica Povedano Panades
Site Name
Complexo Hospitalario Universitario De Santiago
Department Name
Neurology
Principal Investigator Name
Beatrice Canneti Heredia
Principal Investigator Email
canneti.heredia@gmail.com
Contact Person Name
Beatrice Canneti Heredia
Contact Person Email
canneti.heredia@gmail.com
Site Name
Hospital Universitario Y Politecnico La Fe
Department Name
Neurology
Principal Investigator Name
Juan Francisco Vazquez Costa
Principal Investigator Email
vazquez_juacos@gva.es
Contact Person Name
Juan Francisco Vazquez Costa
Contact Person Email
vazquez_juacos@gva.es
Site Name
Hospital Del Mar
Department Name
Neurology
Principal Investigator Name
Miguel Angel Rubio Perez
Principal Investigator Email
marubio@psmar.cat
Contact Person Name
Miguel Angel Rubio Perez
Contact Person Email
marubio@psmar.cat
Site Name
Hospital Carlos III
Department Name
Neurology
Principal Investigator Name
Javier Pedro Mascías Cadavid
Principal Investigator Email
jmascias@yahoo.es
Contact Person Name
Javier Pedro Mascías Cadavid
Contact Person Email
jmascias@yahoo.es
Site Name
Hospital (additional listed site)
Department Name
Neurology

Sweden

Earliest CTIS Part Ii Submission Date
31-03-2026
Latest Decision Or Authorization Date
20-04-2026
Processing Time Days
20
Number Of Sites
2
Number Of Participants
36

Sites

Site Name
Region Stockholm – SLSO
Department Name
ALS Clinic Karolinska University Hospital
Principal Investigator Name
Caroline Ingre
Principal Investigator Email
Caroline.Ingre@regionstockholm.se
Contact Person Name
Caroline Ingre
Site Name
Region Vaesterbotten
Department Name
Department of Neurology A41
Principal Investigator Name
Peter Andersen
Principal Investigator Email
peter.andersen@umu.se
Contact Person Name
Peter Andersen
Contact Person Email
peter.andersen@umu.se

Netherlands

Earliest CTIS Part Ii Submission Date
03-04-2026
Latest Decision Or Authorization Date
20-04-2026
Processing Time Days
17
Number Of Sites
1
Number Of Participants
25

Sites

Site Name
Universitair Medisch Centrum Utrecht
Department Name
Neurology
Principal Investigator Name
Henk-Jan Westeneng
Principal Investigator Email
h.j.westeneng@umcutrecht.nl
Contact Person Name
Henk-Jan Westeneng
Contact Person Email
h.j.westeneng@umcutrecht.nl

Poland

Earliest CTIS Part Ii Submission Date
14-04-2026
Latest Decision Or Authorization Date
23-04-2026
Processing Time Days
9
Number Of Sites
3
Number Of Participants
45

Sites

Site Name
City Clinic Research Sp. z o.o.
Principal Investigator Name
Magdalena Kuźma-Kozakiewicz
Principal Investigator Email
magdalena.kuzma-kozakiewicz@wum.edu.pl
Contact Person Name
Magdalena Kuźma-Kozakiewicz
Site Name
Linden Sp. z o.o. sp.k.
Principal Investigator Name
Jakub Antczak
Principal Investigator Email
jakub.antczak@uj.edu.pl
Contact Person Name
Jakub Antczak
Contact Person Email
jakub.antczak@uj.edu.pl
Site Name
Centrum Medyczne Neuromed Sp. z o.o.
Principal Investigator Name
Pawel Lisiewski
Principal Investigator Email
lisewski.p@gmail.com
Contact Person Name
Pawel Lisiewski
Contact Person Email
lisewski.p@gmail.com

Sponsor

Primary sponsor

Full Name
Ferrer Internacional S.A.
Organisation Type
Pharmaceutical company
Country Of Registered Address
Spain

Contract research organisations

Name
Iqvia Biotech Limited
Responsibilities
Multiple sponsor duties including ECG and French patients reimbursement (various codes listed). Contact: Biotech-EUCTR-Support@iqvia.com
Name
Iqvia Laboratories Limited
Responsibilities
Laboratory activities (sponsor duty code 4). Contact: q2_eu_clinical_trials_information@q2labsolutions.com
Name
Greenphire LLC
Responsibilities
Patient reimbursement and travel arrangements
Name
Marken LLP
Responsibilities
Direct-to-home shipments
Name
Medidata Solutions Inc.
Responsibilities
Data/Medidata (sponsor duty code 7)
Name
Fisher Clinical Services GmbH
Responsibilities
Clinical services / logistics (code 14 indicated)
Name
Primevigilance Limited
Responsibilities
Pharmacovigilance
Name
Bioforum C.D.M.C Ltd.
Responsibilities
Biostatistics services
Name
Redenlab Pty Limited
Responsibilities
Speech assessment
Name
Ppd Inc.
Responsibilities
PK assessment

Third parties

  • {"country":"United Kingdom","full_name":"Iqvia Biotech Limited","duties_or_roles":"codes: 1,11,12,13,15 (value: \"ECG, French patients reimbursement\"),2,5,6,8,9","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Iqvia Laboratories Limited","duties_or_roles":"code: 4","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United States","full_name":"Greenphire LLC","duties_or_roles":"Patient Reimbursement, Travel arrangements","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United States","full_name":"Marken LLP","duties_or_roles":"Direct to home shipments","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Medidata Solutions Inc.","duties_or_roles":"code: 7","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"Germany","full_name":"Fisher Clinical Services GmbH","duties_or_roles":"code: 14","organisation_type":"Pharmaceutical company"}
  • {"country":"Israel","full_name":"Bioforum C.D.M.C Ltd.","duties_or_roles":"Biostatistics services","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Primevigilance Limited","duties_or_roles":"Pharmacovigilance","organisation_type":"Pharmaceutical company"}
  • {"country":"Australia","full_name":"Redenlab Pty Limited","duties_or_roles":"Speech assessment","organisation_type":"Pharmaceutical company"}
  • {"country":"Netherlands","full_name":"TRICALS Foundation Stichting","duties_or_roles":"Patient Recruitment and Site Training services","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United States","full_name":"Ppd Inc.","duties_or_roles":"PK assessment","organisation_type":"Pharmaceutical company"}
  • {"country":"Germany","full_name":"Fisher Clinical Services GmbH (additional address)","duties_or_roles":"code: 14","organisation_type":"Pharmaceutical company"}

Co-sponsors

  • Prilenia Therapeutics B.V.

Investigational products

Investigational Product Name
PRIDOPIDINE
Active Substance
PRIDOPIDINE HYDROCHLORIDE
Modality
Small molecule
Routes Of Administration
ORAL USE
Route
ORAL USE
Orphan Designation
Yes
Maximum Dose
90 mg
Investigational Product Name
Pridopidine placebo
Modality
Other

Related trials

Other published trials that may interest you.