Clinical trial • Phase II • Immunology|Rare Disease

IPTACOPAN for ANCA-associated vasculitis|Granulomatosis with polyangiitis (GPA)|Microscopic polyangiitis (MPA)

Phase II trial of IPTACOPAN for ANCA-associated vasculitis|Granulomatosis with polyangiitis (GPA)|Microscopic polyangiitis (MPA).

Overview

Trial Therapeutic Area
Immunology|Rare Disease
Trial Disease
ANCA-associated vasculitis|Granulomatosis with polyangiitis (GPA)|Microscopic polyangiitis (MPA)
Trial Stage
Phase II
Drug Modality
Small molecule

Key dates

Initial CTIS Submission Date
07-06-2024
First CTIS Authorization Date
17-09-2024

Trial design

Randomised, placebo 0 mg hard gelatin capsule size 0 (placebo to lnp023); standard of care (soc) as per investigator (e.g. rituximab and glucocorticoids as indicated).-controlled Phase II trial in Czechia, Hungary, Netherlands and others.

Randomised
Yes
Comparator
Placebo 0 mg hard gelatin capsule size 0 (placebo to LNP023); Standard of Care (SOC) as per investigator (e.g. rituximab and glucocorticoids as indicated).
Target Sample Size
34
Trial Duration For Participant
336

Eligibility

Recruits 34 Vulnerable populations selected. "Signed informed consent obtained prior to participation in the study." All participants are adults (≥18) and must provide signed informed consent. Country-specific subject information and consent forms are provided..

Vulnerable Population
Vulnerable populations selected. "Signed informed consent obtained prior to participation in the study." All participants are adults (≥18) and must provide signed informed consent. Country-specific subject information and consent forms are provided.

Inclusion criteria

  • {"criterion_text":"- Signed informed consent obtained prior to participation in the study."}
  • {"criterion_text":"- Newly diagnosed or relapsed GPA and MPA (according to the 2022 ACR/EULAR classification criteria for GPA and MPA) requiring treatment with RTX and GC as per investigator's judgement."}
  • {"criterion_text":"- BVAS assessment with ≥1 major item, or ≥3 minor items, or ≥2 renal items at Screening."}
  • {"criterion_text":"- Positive antibody test for anti-proteinase 3 (PR3) or anti-myeloperoxidase (MPO) antibodies at Screening or with history of documented evidence of a positive antibody test."}
  • {"criterion_text":"- Male or female subjects ≥18 years at Screening."}

Exclusion criteria

  • {"criterion_text":"- Other systemic disease which constitutes the primary illness, including but not limited to: eosinophilic granulomatosis with polyangiitis (EGPA), moderate to severe systemic lupus erythematosus, IgA vasculitis (Purpura Schönlein-Henoch), rheumatoid vasculitis, Sjögren's syndrome, anti-glomerular basement membrane (GBM) disease, cryoglobulinemic vasculitis, autoimmune hemolytic anemia, autoimmune lymphoproliferative syndrome or mixed connective tissue disease."}
  • {"criterion_text":"- Alveolar hemorrhage requiring invasive pulmonary ventilation support at Screening."}
  • {"criterion_text":"- Severe kidney disease defined as estimated glomerular filtration rate <15 mL/min/1.73m2, or kidney failure defined as receiving renal replacement therapy such as hemo(dia)filtration, hemo-/peritoneal dialysis, or having received a kidney transplant."}
  • {"criterion_text":"- Received plasma exchange/-pheresis within 12 weeks prior to Screening."}
  • {"criterion_text":"- Received any of the following immunosuppressive, cell depleting or biological therapy (any other immunosuppressive, cell depleting, or biological therapy not listed here must be discussed with the Sponsor): • Received RTX or other B-cell depleting agent within 16 weeks prior to Screening. • Received any of the following biological or alkylating immunosuppressive medications within 12 weeks before screening, including but not limited to: • cyclophosphamide (CYC) • complement inhibitor (such as eculizumab, ravulizumab, avacopan) • anti-tumor necrosis factor • abatacept • tocilizumab • intravenous immunoglobulins • Received any of the following cell depleting agents within 24 weeks before Screening, including but not limited to: • alemtuzumab • antithymocyte globulin • Received azathioprine (AZA), methotrexate (MTX), or mycophenolate (MMF), or any other immunosuppressants with similar half-life within 1 week prior to Day 1. • Received leflunomide (LEF) within 6 weeks prior to Day 1."}

Endpoints

Primary endpoints

  • {"endpoint_text":"- Sustained remission through Week 48 defined as complete remission at Week 24 without major relapse up to Week 48.","definition_or_measurement_approach":"Defined as complete remission at Week 24 without major relapse up to Week 48 (sustained remission through Week 48)."}

Secondary endpoints

  • {"endpoint_text":"- Time to reach BVAS = 0","definition_or_measurement_approach":"Time from baseline to first occurrence of BVAS = 0."}
  • {"endpoint_text":"- Time to major relapse through Week 48","definition_or_measurement_approach":"Time from baseline to a major relapse event up to Week 48."}
  • {"endpoint_text":"- Estimated glomerular filtration rate (eGFR) using the CKD-EI formula, urinary protein excretion and hematuria over 48 weeks.","definition_or_measurement_approach":"Renal function assessed by eGFR (CKD-EPI formula), measurement of urinary protein excretion and presence/degree of hematuria over 48 weeks."}

Recruitment

Planned Sample Size
34
Recruitment Window Months
33
Consent Approach
Signed informed consent obtained prior to participation in the study. Participants are adults (≥18) and provide signed informed consent. Subject information and informed consent forms (L1_ICF Main ICF - Adult) and related documents are available in multiple country/language versions (examples in the file list: English, German, French, Hungarian, Dutch, Spanish, Czech) and country-specific ICFs.

Geography

Total Number Of Sites
30
Total Number Of Participants
44

Czechia

Earliest CTIS Part Ii Submission Date
21-06-2024
Latest Decision Or Authorization Date
13-01-2026
Processing Time Days
571
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Vseobecna Fakultni Nemocnice V Praze
Department Name
#1601: Klinika nefrologie
Contact Person Name
Vladimir Tesar
Contact Person Email
vladimir.tesar@vfn.cz

Hungary

Earliest CTIS Part Ii Submission Date
24-07-2024
Latest Decision Or Authorization Date
15-01-2026
Processing Time Days
540
Number Of Sites
3
Number Of Participants
4

Sites

Site Name
University Of Debrecen
Department Name
#7002: Reumatológiai Klinika
Contact Person Name
Szilvia Szamosi
Contact Person Email
szamosi.szilvia@med.unideb.hu
Site Name
University Of Szeged
Department Name
#7001: Reumatológiai és Immunológiai Klinika
Contact Person Name
László Kovács
Contact Person Email
kovacs.laszlo@med.u-szeged.hu
Site Name
Orszagos Mozgasszervi Intezet
Department Name
#7003: ORFI Campus
Contact Person Name
Anna Bazsó
Contact Person Email
bazsoanna@yahoo.com

Netherlands

Earliest CTIS Part Ii Submission Date
21-06-2024
Latest Decision Or Authorization Date
13-01-2026
Processing Time Days
571
Number Of Sites
1
Number Of Participants
4

Sites

Site Name
Universitair Medisch Centrum Groningen
Department Name
#9001: Rheumatology
Contact Person Name
Bram Rutgers
Contact Person Email
a.rutgers@umcg.nl

Germany

Earliest CTIS Part Ii Submission Date
30-08-2024
Latest Decision Or Authorization Date
15-01-2026
Processing Time Days
503
Number Of Sites
6
Number Of Participants
6

Sites

Site Name
Charite Universitaetsmedizin Berlin KöR
Department Name
#6001: Medizinische Klinik mit Schwerpunkt Nephrologie und Internistische Intensivmedizin
Contact Person Name
Adrian Schreiber
Contact Person Email
adrian.schreiber@charite.de
Site Name
medius KLINIKEN gGmbH
Department Name
#6005: Klinik für Innere Medizin, Rheumatologie, Pneuomologie, Nephrologie und Diabetologie
Contact Person Name
Christian Löffler
Contact Person Email
c.loeffler2@medius-kliniken.de
Site Name
Universitaetsmedizin der Johannes Gutenberg-Universitaet Mainz KöR
Department Name
#6008: I. Medizinische Klinik und Poliklinik
Contact Person Name
Julia Weinmann-Menke
Site Name
Klinikum der Universitaet Muenchen AöR
Department Name
#6004: Medizinische Klinik und Poliklinik IV  Nephrologisches Zentrum
Contact Person Name
Ulf Schönermarck
Site Name
Medical Center - University Of Freiburg
Department Name
#6002: Klinik für Rheumatologie und Klinische Immunologie / Department Innere Medizin
Contact Person Name
Stephanie Finzel
Site Name
Klinikum der Stadt Ludwigshafen am Rhein gGmbH
Department Name
#6006: Med A Klinik/Rheumatologie
Contact Person Name
Raoul Bergner
Contact Person Email
bergnerr@klilu.de

Belgium

Earliest CTIS Part Ii Submission Date
23-08-2024
Latest Decision Or Authorization Date
02-02-2026
Processing Time Days
528
Number Of Sites
2
Number Of Participants
3

Sites

Site Name
Algemeen Ziekenhuis Delta
Department Name
#2002: Nephrology
Contact Person Name
Bart Maes
Contact Person Email
bart.maes@azdelta.be
Site Name
UZ Leuven
Department Name
#2001: Internal Medicine
Contact Person Name
Albrecht Betrains
Contact Person Email
albrecht.betrains@uzleuven.be

Denmark

Earliest CTIS Part Ii Submission Date
29-08-2024
Latest Decision Or Authorization Date
13-01-2026
Processing Time Days
502
Number Of Sites
3
Number Of Participants
5

Sites

Site Name
Aarhus Universitetshospital
Department Name
#4003: Nyremedicinsk Forskning, Nyresygdomme
Contact Person Name
Per Ramløv Ivarsen
Contact Person Email
perivars@rm.dk
Site Name
Rigshospitalet
Department Name
#4001: Afdeling for Nyresygdomme
Contact Person Name
Morten Buus Jørgensen
Site Name
Region Hovedstaden
Department Name
#4002: Afdeling for Nyresygdomme
Contact Person Name
Casper Rydahl
Contact Person Email
casper.rydahl.01@regionh.dk

France

Earliest CTIS Part Ii Submission Date
30-07-2024
Latest Decision Or Authorization Date
19-01-2026
Processing Time Days
538
Number Of Sites
8
Number Of Participants
11

Sites

Site Name
Centre Hospitalier Universitaire De Nantes
Department Name
#5007: Service de Médecine Interne
Contact Person Name
Antoine NEEL
Contact Person Email
antoine.neel@chu-nantes.fr
Site Name
Centre Hospitalier Universitaire D'Angers
Department Name
#5002: Néphrologie
Contact Person Name
Jean-François AUGUSTO
Contact Person Email
jfaugusto@chu-angers.fr
Site Name
Centre Hospitalier Regional Et Universitaire De Brest
Department Name
#5008: Rhumatologie
Contact Person Name
Divi CORNEC
Contact Person Email
divi.cornec@chu-brest.fr
Site Name
Centre Hospitalier Universitaire De Dijon
Department Name
#5005: Département de Médecine Interne et Immunologie Clinique
Contact Person Name
Maxime SAMSON
Contact Person Email
maxime.samson@chu-dijon.fr
Site Name
Centre Hospitalier Regional De Marseille
Department Name
#5009: Néphrologie
Contact Person Name
Noémie JOURDE-CHICHE
Contact Person Email
noemie.jourde@ap-hm.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
#5004: Néphrologie
Contact Person Name
Alexandre KARRAS
Contact Person Email
alexandre.karras@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
#5001: Service de Médecine interne
Contact Person Name
Benjamin TERRIER
Contact Person Email
benjamin.terrier@aphp.fr
Site Name
Centre Hospitalier Universitaire De Toulouse
Department Name
#5006: Service de Médecine interne
Contact Person Name
Grégory PUGNET
Contact Person Email
pugnet.g@chu-toulouse.fr

Spain

Earliest CTIS Part Ii Submission Date
21-08-2024
Latest Decision Or Authorization Date
15-01-2026
Processing Time Days
512
Number Of Sites
3
Number Of Participants
5

Sites

Site Name
Clinica Universidad De Navarra
Department Name
#1102: Servicio de Reumatología
Contact Person Name
Miguel Angel Suarez Santisteban
Site Name
Hospital Universitario La Paz
Department Name
#1101: Servicio de Reumatología
Contact Person Name
Eugenio De Miguel Mendieta
Site Name
Hospital Virgen Del Puerto
Department Name
#1103: Servicio de Nefrología
Contact Person Name
Enrique Ornilla Laraudogoitia
Contact Person Email
eornilla@unav.es

Austria

Earliest CTIS Part Ii Submission Date
24-07-2024
Latest Decision Or Authorization Date
16-01-2026
Processing Time Days
541
Number Of Sites
3
Number Of Participants
4

Sites

Site Name
Medical University Of Vienna
Department Name
#1001
Contact Person Name
Clemens Scheinecker
Site Name
Medical University Of Graz
Department Name
#1002
Contact Person Name
Jens Thiel
Contact Person Email
jens.thiel@medunigraz.at
Site Name
Medizinische Universitaet Innsbruck
Department Name
#1003: Neurologie
Contact Person Name
Andreas Kronbichler

Sponsor

Primary sponsor

Full Name
Novartis Pharma AG
Organisation Type
Pharmaceutical company
Country Of Registered Address
Switzerland

Contract research organisations

Name
4g Clinical LLC
Responsibilities
code 3
Name
Q Squared Solutions LLC
Responsibilities
code 4
Name
Syneos Health Inc.
Responsibilities
code 1
Name
Icon Clinical Research Limited
Responsibilities
code 1
Name
IQVIA Limited
Responsibilities
code 1
Name
Parexel International (IRL) Limited
Responsibilities
code 12
Name
Veeda Clinical Research Limited
Responsibilities
code 15 (PK analysis); code 4
Name
Mag. Andreas Raffeiner GmbH
Responsibilities
code 8

Third parties

  • {"country":"United States","full_name":"4g Clinical LLC","duties_or_roles":"code 3","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United States","full_name":"Q Squared Solutions LLC","duties_or_roles":"code 4","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United States","full_name":"Syneos Health Inc.","duties_or_roles":"code 1","organisation_type":"Pharmaceutical company"}
  • {"country":"Ireland","full_name":"Icon Clinical Research Limited","duties_or_roles":"code 1","organisation_type":"Pharmaceutical company"}
  • {"country":"Austria","full_name":"Mag. Andreas Raffeiner GmbH","duties_or_roles":"code 8","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"IQVIA Limited","duties_or_roles":"code 1","organisation_type":"Pharmaceutical company"}
  • {"country":"Ireland","full_name":"Parexel International (IRL) Limited","duties_or_roles":"code 12","organisation_type":"Pharmaceutical company"}
  • {"country":"India","full_name":"Veeda Clinical Research Limited","duties_or_roles":"code 15 (PK analysis); code 4","organisation_type":"Pharmaceutical company"}

Investigational products

Investigational Product Name
IPTACOPAN
Active Substance
IPTACOPAN
Modality
Small molecule
Routes Of Administration
ORAL
Route
ORAL
Maximum Dose
400 mg/day
Investigational Product Name
Placebo 0 mg hard gelatin capsule size 0, (placebo to LNP023)
Modality
Other
Routes Of Administration
Oral (hard gelatin capsule)
Route
ORAL
Starting Dose
0 mg
Combination Treatment
Yes

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