Clinical trial • Phase III • Neurology

ZOREVUNERSEN SODIUM for Dravet syndrome

Phase III trial of ZOREVUNERSEN SODIUM for Dravet syndrome. Randomised, sham (sham control procedure).. 150 participants.

Overview

Trial Therapeutic Area
Neurology
Trial Disease
Dravet syndrome
Trial Stage
Phase III
Drug Modality
Oligonucleotide
Paediatric Trial
Yes
Orphan Drug
Yes

Key dates

Initial CTIS Submission Date
17-02-2025
First CTIS Authorization Date
30-06-2025

Trial design

Randomised, sham (sham control procedure). Phase III trial across 30 sites in Sweden, Poland, Spain and others.

Randomised
Yes
Comparator
Sham (sham control procedure).
Target Sample Size
150
Trial Duration For Participant
364

Eligibility

Recruits 150 paediatric patients.

Vulnerable Population
Paediatric population selected (patients ≥2 and <18 years). Consent/assent handling: patient and/or authorized representative must be willing and able to give informed consent/assent; caregiver involvement required for protocol compliance. Study-specific parental/legal guardian ICFs and age-appropriate assent forms are provided (including assent for older children/teens, parental/legal guardian ICFs, additional caregiver ICFs, and documents for participants turning 18). eConsent materials and translated documents are available for country-specific use.

Inclusion criteria

  • {"criterion_text":"-Patient and/or authorized representative must be willing and able to give informed consent/assent and any authorizations required by local law for participation in the study."}
  • {"criterion_text":"-Patient and their caregiver must be willing and able (in the Investigator’s opinion) to comply with all protocol requirements."}
  • {"criterion_text":"-At signing of consent/assent, patient must be ≥2 and <18 years of age."}
  • {"criterion_text":"-Patient must have a clinical diagnosis of DS confirmed by the Epilepsy Study Consortium, Inc. (ESCI) and as defined by: Onset, prior to 12 months of age, of recurrent focal with motor signs, hemiclonic, or generalized tonic-clonic seizures, which are often prolonged and triggered by hyperthermia. No past history of causal magnetic resonance imaging (MRI) lesion (past MRI or study-associated MRI not required to confirm absence of lesion). No other known etiology causing clinical DS manifestations. Normal development at seizure onset."}
  • {"criterion_text":"-Patient must have a documented pathogenic, likely pathogenic variant, or variant of uncertain significance in the sodium voltage-gated channel type 1 alpha subunit (SCN1A) gene. Patients who have SCN1A testing results of Negative (no variants identified) cannot be randomized."}
  • {"criterion_text":"-Experiences the required number of major motor seizures during the 6-week Observation Period. Seizure types included in counts are Hemiclonic, Focal with Motor Signs, Focal to Bilateral Tonic-Clonic, Generalized Tonic-Clonic, Tonic, Tonic/Atonic (Drop Attacks with fall or risk of fall), and Bilateral Clonic."}
  • {"criterion_text":"-Patient must have used at least 2 prior interventions for seizures. These can include anti-seizure medications (ASMs), ketogenic diet and/or vagus nerve stimulation (VNS) with either lack of adequate seizure control or discontinued due to an AE(s). These interventions can be ongoing therapies."}
  • {"criterion_text":"-Patient must be taking at least one ASM. Benzodiazepines or ASMs used on a standing basis (i.e., not as needed [PRN]) for any indication will be considered an ASM."}
  • {"criterion_text":"-All maintenance ASMs and interventions for seizures (i.e., ketogenic diet or VNS), as well as any marijuana- or cannabinoid-based products, must have been stable (unless adjusted for weight) during the Baseline Period. Felbamate must have been stable (unless adjusted for weight) for at least 6 months prior to Screening Visit A and during the Baseline Period. VNS implantation must have occurred at least 6 months prior to Screening Visit A. Rescue ASMs used on an as needed basis do not need to be stable."}

Exclusion criteria

  • {"criterion_text":"-Patient has documented variant in the SCN1A gene associated with gain-of-function potentially including but not limited to: Ala23Glu, Thr162Ile, Arg1636Gln, Thr226Met, Ile236Val, Val250Leu, Leu263Val, Thr398Met, Ala420Val, Val422Leu, Thr1174Ser, Trp1204Arg, Pro1345Ser, Ile1483Met, Gln1489Lys, Ile1498Thr, Ile1498Met, Phe1499Leu, Met1500Val, Arg1575Cys, Val1611Phe, Leu1624Pro, Arg1636Gln, Arg1648Cys, Leu1649Gln, Leu1660Ile, Phe1661Leu, Leu1670Trp, Gly1674Arg, Phe1774Ser, or Asp1866Tyr."}
  • {"criterion_text":"-Patient has a diagnostic result in a gene other than SCN1A on the epilepsy gene screening panel. For genes associated with dominant inheritance, one heterozygous pathogenic or likely pathogenic variant is exclusionary. For genes associated with recessive inheritance, biallelic pathogenic or likely pathogenic variant(s) are exclusionary. This includes homozygous variants and compound heterozygous variants. Results consistent with carrier status are not exclusionary."}
  • {"criterion_text":"-Patient is currently treated with a maintenance ASM acting primarily as a sodium channel blocker, including but not limited to phenytoin, carbamazepine, oxcarbazepine, lamotrigine, lacosamide, rufinamide, or cenobamate, given the mechanism of action of zorevunersen."}
  • {"criterion_text":"-Patient is currently treated with neuromodulation techniques (e.g., responsive neurostimulation, deep brain stimulation, or transcranial magnetic stimulation), with the exception of VNS."}
  • {"criterion_text":"-Patient has emergence of a new seizure type or reemergence of a past seizure type (seizure types that last occurred more than 12 months before Screening Visit A) during the Baseline Period, or has more than 1 hospitalization for seizures during the Baseline Period."}
  • {"criterion_text":"-Patient has a spinal deformity or other condition that may alter the free flow of CSF or has an implanted CSF drainage shunt. This does not exclude patients with scoliosis or spinal rods if, in the judgement of the Investigator, lumbar puncture can be performed and there is free flow of CSF."}

Endpoints

Primary endpoints

  • {"endpoint_text":"-Percent change from baseline in major motor seizure frequency (number per 28 days) in patients receiving zorevunersen as compared with sham from Week 16 to Week 28 (consisting of three 4 week intervals).","definition_or_measurement_approach":"Percent change from baseline in major motor seizure frequency measured as number of major motor seizures per 28 days comparing zorevunersen versus sham between Week 16 and Week 28. Major motor seizures are defined in the protocol as: hemiclonic, focal with motor signs, focal to bilateral tonic-clonic, generalized tonic-clonic, tonic, tonic/atonic (drop attacks with fall or risk of fall), and bilateral clonic."}

Secondary endpoints

  • {"endpoint_text":"-Percent change from baseline in major motor seizure frequency (number per 28 days) in patients receiving zorevunersen as compared with sham at each visit from Week 16 to Week 52 (consisting of nine 4 week intervals).","definition_or_measurement_approach":"Percent change from baseline in major motor seizure frequency measured at each visit from Week 16 through Week 52 (nine 4-week intervals); comparisons of zorevunersen versus sham."}
  • {"endpoint_text":"-Net treatment benefit across multiple Vineland 3 outcomes, assessed as change from baseline, in patients receiving zorevunersen as compared with sham at Week 52.","definition_or_measurement_approach":"Net treatment benefit evaluated across multiple Vineland-3 outcomes as change from baseline at Week 52 comparing zorevunersen versus sham."}
  • {"endpoint_text":"-Change from baseline in subdomain scores on the Vineland-3 in patients receiving zorevunersen as compared with sham at Week 52.","definition_or_measurement_approach":"Change from baseline in Vineland-3 subdomain scores at Week 52 comparing treatment versus sham."}

Recruitment

Registry Or Advocacy Recruitment
True, Epilepsy Study Consortium Inc.
Digital Remote Recruitment
True, includes eConsent (electronic consent) materials, eConsent videos/screenshots, online patient pre-screening website content and ePR website placeholders (country-specific eConsent and online recruitment materials referenced).
Planned Sample Size
150
Recruitment Window Months
30
Consent Approach
Informed consent obtained from patient and/or authorized representative; assent obtained from minors per age-appropriate assent forms. Study uses parental/legal guardian ICFs, assent forms (including assent over 12), additional caregiver ICFs, 'turning 18' materials for participants who reach adulthood during study, and eConsent materials. Documents available in multiple languages (English, French, Spanish, Italian, German, Polish and country-specific versions).

Methods

  • K1_Recruitment arrangements / recruitment procedure (study-level recruitment procedure document) — outlines overall recruitment process and channels.
  • Parent-caregiver brochure (K2) — patient-facing printed/online material targeted to parents and caregivers; country/language-specific versions available (e.g., ESP, ITA, FRA, SWE).
  • Physician referral letter (K2) — targeted to clinicians to facilitate referrals.
  • Website content / ePR / patient pre-screening website content — online recruitment and pre-screening channel (ePR website placeholders and patient pre-screening website documents listed).
  • Lumbar puncture animation storyboard — educational multimedia to explain intrathecal procedure to participants/parents.
  • eConsent materials and eConsent videos/screenshots — digital consent channel and supporting materials.
  • Patient materials (study summaries, patient ID card, thank you cards) — patient-facing collateral to support recruitment and retention.

Geography

Total Number Of Sites
30
Total Number Of Participants
35

Sweden

Earliest CTIS Part Ii Submission Date
28-07-2025
Latest Decision Or Authorization Date
13-08-2025
Processing Time Days
16
Number Of Sites
3
Number Of Participants
6

Sites

Site Name
Queen Silvia Childrens Hospital - Sahlgrenska University Hospital - Vaestra Goetalandsregionen
Department Name
Drottning Silvias barnsjukhus, Sahlgrenska Universitetssjukhuset
Contact Person Name
Tove Hallböök
Contact Person Email
tove.hallbook@vgregion.se
Site Name
Region Skane Skanes Universitetssjukhus
Department Name
Skånes Universitetssjukhus
Contact Person Name
Erik Eklund
Contact Person Email
erik.eklund@skane.se
Site Name
Karolinska University Hospital
Department Name
Karolinska Universitetssjukhuset
Contact Person Name
Ronny Wickström
Contact Person Email
ronny.wickstrom@ki.se

Poland

Earliest CTIS Part Ii Submission Date
11-08-2025
Latest Decision Or Authorization Date
08-09-2025
Processing Time Days
28
Number Of Sites
3
Number Of Participants
9

Sites

Site Name
Uniwersytecki Szpital Kliniczny W Poznaniu
Department Name
Oddział Kliniczny Neurologii Dzieci i Młodzieży
Contact Person Name
Barbara Steinborn
Contact Person Email
bstein@ump.edu.pl
Site Name
Instytut Centrum Zdrowia Matki Polki
Department Name
Klinika Neurologii Rozwojowej i Epileptologii
Contact Person Name
Łukasz Przysło
Contact Person Email
lukasz.przyslo@iczmp.edu.pl
Site Name
Uniwersyteckie Centrum Kliniczne
Department Name
Klinika Neurologii Rozwojowej
Contact Person Name
Maria Mazurkiewicz- Bełdzińska
Contact Person Email
mmazur@gumed.edu.pl

Spain

Earliest CTIS Part Ii Submission Date
24-01-2025
Latest Decision Or Authorization Date
30-06-2025
Processing Time Days
157
Number Of Sites
5
Number Of Participants
3

Sites

Site Name
Hospital Universitario Y Politecnico La Fe
Department Name
Neurology
Contact Person Name
Vicente Villanueva Haba
Contact Person Email
vevillanuevah@yahoo.es
Site Name
Hospital Ruber Internacional
Department Name
Neurology
Contact Person Name
Antonio Gil-Nagel Rein
Contact Person Email
agnagel@neurologiaclinica.es
Site Name
Hospital Blua Sanitas Valdebebas
Department Name
Neurology
Contact Person Name
Ángel Aledo Serrano
Contact Person Email
as.aledo@gmail.com
Site Name
Hospital De La Santa Creu I Sant Pau
Department Name
Neurology
Contact Person Name
Alba Sierra Marcos
Contact Person Email
asierram@santpau.cat
Site Name
Clinica Universidad De Navarra
Department Name
Paediatric Neurology
Contact Person Name
Rocío Sánchez-Carpintero Abad
Contact Person Email
rsanchezc@unav.es

Italy

Earliest CTIS Part Ii Submission Date
06-08-2025
Latest Decision Or Authorization Date
03-09-2025
Processing Time Days
28
Number Of Sites
5
Number Of Participants
2

Sites

Site Name
Fondazione Policlinico Universitario Agostino Gemelli IRCCS
Department Name
Neurologia Infantile
Contact Person Name
Domenica Immacolata Battaglia
Site Name
IRCCS Istituto Giannina Gaslini
Department Name
Neurologia Pediatrica e Malattie Muscolari
Contact Person Name
Pasquale Striano
Contact Person Email
pasquale.striano@unige.it
Site Name
ASST Fatebenefratelli Sacco
Department Name
Neurologia Pediatrica
Contact Person Name
Silvia Masnada
Site Name
Azienda Ospedaliera Universitaria Meyer IRCCS
Department Name
Neuroscience and Human Genetics Department - Neurologia Peditrica
Contact Person Name
Renzo Guerrini
Contact Person Email
renzo.guerrini@meyer.it
Site Name
Ospedale Pediatrico Bambino Gesu
Department Name
Neurologia dell'Epilessia e Disturbi del movimento
Contact Person Name
Nicola Specchio
Contact Person Email
nicola.specchio@opbg.net

Germany

Earliest CTIS Part Ii Submission Date
25-08-2025
Latest Decision Or Authorization Date
08-09-2025
Processing Time Days
14
Number Of Sites
7
Number Of Participants
12

Sites

Site Name
Universitaetsklinikum Bonn AöR
Department Name
Neuropädiatrie und Sozialpädiatrisches Zentrum
Contact Person Name
Walid Fazeli
Contact Person Email
studienzentrale-szb@ukbonn.de
Site Name
Medical Center - University Of Freiburg
Department Name
KJK Neuropaediatrie und Muskelerkrankungen
Contact Person Name
Jan Schönberger
Site Name
Gesellschaft Fuer Epilepsieforschung
Department Name
Department for Epileptology
Contact Person Name
Tilman Polster
Contact Person Email
tilman.polster@mara.de
Site Name
Universitaetsklinikum Heidelberg AöR
Department Name
paedKiiS
Contact Person Name
Steffen Syrbe
Site Name
Ludwig-Maximilians-Universitaet Muenchen
Department Name
Department of Pediatric Neurology, Developmental Medicine and Social Pediatrics
Contact Person Name
Ingo Borggraefe
Site Name
Charite Universitaetsmedizin Berlin KöR
Department Name
Klinik für Pädiatrie m.S. Neruologie
Contact Person Name
Angela Kaindl
Contact Person Email
angela.kaindl@charite.de
Site Name
Goethe University Frankfurt
Department Name
Klinik für Kindee und Jugendmedizin
Contact Person Name
Susanne Schubert-Bast

France

Earliest CTIS Part Ii Submission Date
18-07-2025
Latest Decision Or Authorization Date
28-07-2025
Processing Time Days
10
Number Of Sites
7
Number Of Participants
3

Sites

Site Name
Centre Hospitalier Regional De Marseille
Department Name
Service de Neurométabolisme Pédiatrique
Contact Person Name
Mathieu MILH
Contact Person Email
mathieu.milh@ap-hm.fr
Site Name
Les Hopitaux Universitaires De Strasbourg
Department Name
Service Neurologie Pédiatrique
Contact Person Name
Anne DE SAINT-MARTIN
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Service Neurologie Pédiatrique
Contact Person Name
Rima EL NABBOUT - TARANTINO
Contact Person Email
rima.nabbout@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Service Neurologie Pédiatrique
Contact Person Name
Stéphane AUVIN
Contact Person Email
stephane.auvin@aphp.fr
Site Name
Hospices Civils De Lyon
Department Name
Service Epileptologie Clinique, Troubles du Sommeil, Neurologie Fonctionnelle de l’Enfant
Contact Person Name
Joseph TOULOUSE
Contact Person Email
joseph.toulouse@chu-lyon.fr
Site Name
Centre Hospitalier Regional Universitaire De Tours
Department Name
Service Neuropédatrie et Handicaps
Contact Person Name
Maximilien PERIVIER
Contact Person Email
m.perivier@chu-tours.fr
Site Name
Hospices Civils De Lyon (additional listing)
Department Name
Service Epileptologie Clinique, Troubles du Sommeil, Neurologie Fonctionnelle de l’Enfant

Sponsor

Primary sponsor

Full Name
Stoke Therapeutics Inc.
Organisation Type
Pharmaceutical company
Country Of Registered Address
United States

Contract research organisations

Name
IQVIA Limited
Responsibilities
Operational/execution roles (sponsorDuties codes: 1,12,13,2,3,5,8) and EU clinical trials information contact (eu_clinical_trials_information@iqvia.com).
Name
PPD Development LP
Responsibilities
Sample analysis (PK, CSF bioA, ADA)
Name
PPD International Holdings LLC
Responsibilities
Site services (siteservices.eu@ppdi.com)
Name
Fisher Clinical Services GmbH / Fisher Clinical Services UK Limited
Responsibilities
Clinical packaging/ancillary kits and logistics (contacts provided)

Third parties

  • {"country":"Germany","full_name":"Fisher Clinical Services GmbH","duties_or_roles":"sponsorDuties codes: 14","organisation_type":"Pharmaceutical company"}
  • {"country":"Australia","full_name":"Cogstate Limited","duties_or_roles":"Rating Scales Mgmt, Vineland-3 Central Rating & Cognitive Assessments","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Eresearchtechnology Inc.","duties_or_roles":"ECG Central Reader","organisation_type":"Pharmaceutical company"}
  • {"country":"Finland","full_name":"Blueprint Genetics Oy","duties_or_roles":"Genetic testing","organisation_type":"Hospital/Clinic/Other health care facility"}
  • {"country":"United States","full_name":"PPD Development LP","duties_or_roles":"Sample analysis (PK, CSF bioA, ADA)","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"IQVIA Limited","duties_or_roles":"sponsorDuties codes: 1, 12, 13, 2, 3, 5, 8","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Medical Equipment Supplies And Management Limited","duties_or_roles":"Equipment","organisation_type":"Pharmaceutical company"}
  • {"country":"Belgium","full_name":"Icometrix","duties_or_roles":"MRI scan reading","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Quest Diagnostics Nichols Institute Inc.","duties_or_roles":"Exploratory CSF and Serum Protein Characterization","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United States","full_name":"Red Nucleus Solutions LLC","duties_or_roles":"Caregiver assessment","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Q Squared Solutions Limited","duties_or_roles":"sponsorDuties code: 4","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"France","full_name":"Cerba","duties_or_roles":"CSF Protein Total","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United Kingdom","full_name":"Fisher Clinical Services UK Limited","duties_or_roles":"Ancillary kits management","organisation_type":"Pharmaceutical company"}
  • {"country":"Belgium","full_name":"PPD International Holdings LLC","duties_or_roles":"sponsorDuties code: 4","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Prometrika LLC","duties_or_roles":"Biostats, DSMC (data and safety monitoring committee); codes 10, 6, 7","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Gray Consulting Inc.","duties_or_roles":"Concierge Services and Patient payment","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Epilepsy Study Consortium Inc.","duties_or_roles":"Diagnostic Review – Seizure ID and Diagnostic Review","organisation_type":"Pharmaceutical company"}

Investigational products

Investigational Product Name
STK-001
Active Substance
ZOREVUNERSEN SODIUM
Modality
Oligonucleotide
Routes Of Administration
INTRATHECAL USE
Route
Intrathecal
Authorisation Status
prodAuthStatus: 1
Orphan Designation
Yes
Maximum Dose
225 mg (maxTotalDoseAmount)
Investigational Product Name
STK-001
Active Substance
ZOREVUNERSEN SODIUM
Modality
Oligonucleotide
Routes Of Administration
INTRATHECAL USE
Route
Intrathecal
Authorisation Status
prodAuthStatus: 1
Orphan Designation
Yes
Maximum Dose
140 mg (maxTotalDoseAmount)

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