Clinical trial • Phase I/II • Oncology

ZILOVERTAMAB VEDOTIN for B-cell acute lymphoblastic leukemia|Diffuse large B-cell lymphoma|Burkitt lymphoma|Neuroblastoma|Ewing sarcoma

Phase I/II trial of ZILOVERTAMAB VEDOTIN for B-cell acute lymphoblastic leukemia|Diffuse large B-cell lymphoma|Burkitt lymphoma|Neuroblastoma|Ewing sarcom…

Overview

Trial Therapeutic Area
Oncology
Trial Disease
B-cell acute lymphoblastic leukemia|Diffuse large B-cell lymphoma|Burkitt lymphoma|Neuroblastoma|Ewing sarcoma
Trial Stage
Phase I/II
Drug Modality
ADC|Monoclonal antibody
Paediatric Trial
Yes

Key dates

Initial CTIS Submission Date
29-11-2023
First CTIS Authorization Date
15-04-2024

Trial design

adaptive Phase I/II trial across 26 sites in Italy, Slovakia, Spain and others.

Adaptive
True - Part 1 includes a dose-escalation design evaluating dose-limiting toxicities (DLTs) with dose modifications and interim safety assessments (adaptive escalation based on observed DLTs/AEs).
Single Multiple Or Escalation Dose Combined
Yes
Target Sample Size
63

Eligibility

Recruits 63 paediatric patients.

Vulnerable Population
The trial includes pediatric and young adult participants (population includes birth through <18 years for some indications and up to 25 years for Ewing sarcoma). Vulnerable populations are selected (isVulnerablePopulationSelected = true). Consent/assent handling: parental/legal guardian consent is required for minors; age-appropriate assent and consent documents are provided (numerous country-specific informed consent and assent forms listed for age groups such as 02-05 yr, 06-09 yr, 06-11 yr, 10-14 yr, 12-17 yr, 13-17 yr, and versions for parent/guardian and adult participants). Country- and language-specific consent and assent materials are available as reflected in the submitted ICF/assent documents.

Inclusion criteria

  • {"criterion_text":"- For hematological malignancies: Confirmed diagnosis of B-precursor B-ALL or DLBCL/Burkitt lymphoma according to World Health Organization (WHO) classification of neoplasms of the lymphoid tissues (As of protocol Amendment 4, in countries in the European Economic Area [EEA], the substudy will not enroll participants with hematological malignancies)\n- For solid tumor malignancies: Histologically confirmed diagnosis of neuroblastoma or Ewing sarcoma (As of protocol Amendment 4, in countries in the European Economic Area [EEA], the substudy will only enroll participants with diagnosis of Ewing sarcoma)"}

Exclusion criteria

  • {"criterion_text":"- Has history of solid organ transplant.\n- Has received prior radiotherapy within 4 weeks of start of study intervention. Participants must have recovered from all radiation-related toxicities.\n- Has ongoing, chronic corticosteroid therapy (exceeding 10 mg daily of prednisone equivalent). Prednisone equivalent dosing must have been stable for at least 4 weeks before Cycle 1 Day 1 (C1D1).\n- Has received a strong cytochrome P450 3A4 (CYP3A4) inhibitor within 7 days or a strong CYP3A4 inducer within 14 days before the start of study intervention or expected requirement for chronic use of a strong CYP3A4 inhibitor or inducer during the study intervention period and for 30 days after the last dose of study intervention\n- Has received prior systemic anticancer therapy including investigational agents within 4 weeks before the first dose of study intervention (except for prophylactic intrathecal chemotherapy and/or cytoreductive therapy with steroids/hydroxyurea.\n- Has received a live or live-attenuated vaccine within 30 days before the first dose of study intervention. Administration of killed vaccines is allowed.\n- Has received an investigational agent or has used an investigational device within 4 weeks prior to study intervention administration.\n- Has known additional malignancy that is progressing or has required active treatment within the past 1 year.\n- Has active infection requiring systemic therapy.\n- Has known history of Hepatitis B or known active Hepatitis C virus infection.\n- Participants who have not adequately recovered from major surgery or have ongoing surgical complications.\n- Has clinically significant (ie, active) cardiovascular disease.\n- Known history of liver cirrhosis.\n- Has ongoing Grade >1 peripheral neuropathy.\n- Has demyelinating form of Charcot-Marie-Tooth disease.\n- Has been diagnosed with Down syndrome.\n- Has ongoing graft-versus-host disease (GVHD) of any grade or receiving systemic GVHD treatment or prophylaxis.\n- Has history of human immunodeficiency virus (HIV) infection.\n- Has contraindication or hypersensitivity to any of the study intervention components."}

Endpoints

Primary endpoints

  • {"endpoint_text":"- Part 1: Number of Participants from 1 to <18 years of Age Who Experience a Dose-Limiting Toxicity (DLT)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1: Number of Participants from 1 to <18 years of Age Who Experience One or More Adverse Events (AEs)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1: Number of Participants from 1 to <18 years of Age Who Discontinue Study Treatment Due to AEs","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1: Number of Participants from 1 to <18 years of Age Who Receive Dose Modification Due to AEs","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Objective Response (OR) for Participants with B-Cell Acute Lymphoblastic Leukemia (B-ALL)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: OR for Participants with Diffuse Large B-Cell Lymphoma (DLBCL)/Burkitt Lymphoma, Neuroblastoma, and Ewing Sarcoma","definition_or_measurement_approach":""}

Secondary endpoints

  • {"endpoint_text":"- Part 1 and Part 2: Area Under the Curve (AUC) of Total Antibody","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Maximum Plasma Concentration (Cmax) of Total Antibody","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Plasma Trough Concentration (Ctrough) of Total Antibody","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Apparent Terminal Half-life (t1/2) of Total Antibody","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: AUC of Antibody-Drug Conjugate (ADC)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Cmax of Antibody-Drug Conjugate (ADC)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Ctrough of Antibody-Drug Conjugate (ADC)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: t1/2 of Antibody-Drug Conjugate (ADC)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: AUC of Monomethyl Auristatin E (MMAE)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Cmax of Monomethyl Auristatin E (MMAE)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Ctrough of Monomethyl Auristatin E (MMAE)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: t1/2 of Monomethyl Auristatin E (MMAE)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 2: Number of Participants Who Experience One or More Adverse Events (AEs)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 2: Number of Participants Who Discontinue Study Treatment Due to AEs","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 2: Number of Participants Who Receive Dose Modification Due to AEs","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Incidence of Antidrug antibodies (ADAs) to Zilovertamab Vedotin","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Duration of Response (DOR)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Percentage of Participants with DLBCL/Burkitt Lymphoma Who Receive Stem Cell Transplant (SCT)","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Percentage of Participants with B-ALL Who Receive SCT","definition_or_measurement_approach":""}
  • {"endpoint_text":"- Part 1 and Part 2: Percentage of Participants with B-ALL Who Receive Chimeric Antigen Receptor T (CAR-T)","definition_or_measurement_approach":""}

Recruitment

Planned Sample Size
63
Recruitment Window Months
60
Consent Approach
Informed consent is obtained from parents/legal guardians for minors; age-appropriate assent forms are provided for children and adolescents. Multiple country-specific consent and assent forms are submitted (documents for adult consent, parent/guardian consent, and assent for age bands such as 02-05 yr, 06-09 yr, 06-11 yr, 10-14 yr, 12-17 yr, 13-17 yr). Optional/ancillary consent documents (e.g., pregnancy follow-up, genetic consent, data privacy forms) are also provided. Consent materials are available in country-specific languages as indicated by the submitted ICF/assent documents.

Geography

Total Number Of Sites
26
Total Number Of Participants
50

Italy

Earliest CTIS Part Ii Submission Date
21-12-2023
Latest Decision Or Authorization Date
11-11-2025
Processing Time Days
691
Number Of Sites
3
Number Of Participants
8

Sites

Site Name
Azienda Ospedaliera Universitaria Citta' Della Salute E Della Scienza Di Torino
Department Name
S.C. Oncoematologia Pediatrica
Contact Person Name
Franca Fagioli
Contact Person Email
franca.fagioli@unito.it
Site Name
Bambino Gesu Childrens Hospital
Department Name
Dipartimento di Onco-Ematologia e Terapia Cellulare e Genica
Contact Person Name
Franco Locatelli
Contact Person Email
franco.locatelli@opbg.net
Site Name
Fondazione IRCCS Istituto Nazionale Dei Tumori
Department Name
S.C. Pediatria Oncologica
Contact Person Name
Michela Casanova

Slovakia

Earliest CTIS Part Ii Submission Date
14-03-2025
Latest Decision Or Authorization Date
22-10-2025
Processing Time Days
222
Number Of Sites
1
Number Of Participants
1

Sites

Site Name
Narodny Ustav Detskych Chorob
Department Name
Klinika detskej hematologie a onkologie
Contact Person Name
Alexandra Kolenova
Contact Person Email
alexandra.kolenova@nudch.eu

Spain

Earliest CTIS Part Ii Submission Date
14-03-2024
Latest Decision Or Authorization Date
05-03-2026
Processing Time Days
722
Number Of Sites
4
Number Of Participants
9

Sites

Site Name
Hospital Universitario Y Politecnico La Fe
Department Name
Onco hematologia pediatrica
Contact Person Name
Antonio Juan Ribelles
Contact Person Email
juan_antrib@gva.es
Site Name
Hospital Infantil Universitario Nino Jesus
Department Name
Pediatric
Contact Person Name
Alba Rubio San Simón
Contact Person Email
alba.rubio@salud.madrid.org
Site Name
Sant Joan De Deu Barcelona Hospital
Department Name
Oncological Pediatric Unit
Contact Person Name
Jaume Mora Graupera
Contact Person Email
jaume.mora@sjd.es
Site Name
Hospital Universitari Vall D Hebron
Department Name
Pediatric Oncology and Hematology Department
Contact Person Name
Raquel Hladun Alvaro
Contact Person Email
raquel.hladun@vallhebron.cat

Netherlands

Earliest CTIS Part Ii Submission Date
18-03-2024
Latest Decision Or Authorization Date
17-02-2026
Processing Time Days
702
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
Prinses Maxima Centrum voor Kinderoncologie B.V.
Department Name
Kinderoncologie
Contact Person Name
Natasha van Eijkelenburg

Sweden

Earliest CTIS Part Ii Submission Date
14-03-2024
Latest Decision Or Authorization Date
05-02-2026
Processing Time Days
694
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Queen Silvia Childrens Hospital - Sahlgrenska University Hospital - Vastra Gotalandsregionen
Department Name
Barncancercentrum
Contact Person Name
Karin Mellgren
Contact Person Email
karin.mellgren@vgregion.se

France

Earliest CTIS Part Ii Submission Date
23-02-2024
Latest Decision Or Authorization Date
22-01-2026
Processing Time Days
699
Number Of Sites
5
Number Of Participants
8

Sites

Site Name
Centre Hospitalier Universitaire De Nantes
Department Name
Oncologie-Hématologie pédiatrique
Contact Person Name
Morgane Cleirec
Contact Person Email
morgane.cleirec@chu-nantes.fr
Site Name
Centre Hospitalier Universitaire De Bordeaux
Department Name
Unité d'onco- hematologie pédiatrique
Contact Person Name
Stéphane Ducassou
Site Name
Centre Leon Berard
Department Name
Institut d’Hématologie et d’Oncologie Pédiatrique(IHOPe)
Contact Person Name
Nadege Corradini
Contact Person Email
nadege.corradini@ihope.fr
Site Name
Assistance Publique Hopitaux De Marseille
Department Name
Service d'immunologie hématologie et Oncologie Pédiatrique
Contact Person Name
Nicolas André
Contact Person Email
nicolas.andre@ap-hm.fr
Site Name
Institut Gustave Roussy
Department Name
Cancérologie Enfant et Adolescent
Contact Person Name
Pablo Berlanga

Germany

Earliest CTIS Part Ii Submission Date
14-03-2024
Latest Decision Or Authorization Date
10-02-2026
Processing Time Days
699
Number Of Sites
5
Number Of Participants
4

Sites

Site Name
Universitaet Muenster
Department Name
Pädiatrische Hämatologie und Onkologie
Contact Person Name
Claudia Rössig
Contact Person Email
paedonc@ukmuenster.de
Site Name
Justus-Liebig-Universitaet Giessen
Department Name
Zentrum für Kinderheilkunde
Contact Person Name
Christine Mauz-Körholz
Site Name
Universitaetsklinikum Tuebingen AöR
Department Name
Abteilung für päd. Hämatologie und Onkologie
Contact Person Name
Martin Ebinger
Site Name
University Hospital Cologne AöR
Department Name
Pädiatrische Onkologie und Hämatologie
Contact Person Name
Matthias Fischer
Contact Person Email
matthias.fischer@uk-koeln.de
Site Name
Charite Universitaetsmedizin Berlin KöR
Department Name
Klinik für Pädiatrie m. S. Onkologie und Hämatologie
Contact Person Name
Anne Thorwarth
Contact Person Email
cathrin.schmeller@charite.de

Hungary

Earliest CTIS Part Ii Submission Date
22-02-2024
Latest Decision Or Authorization Date
13-02-2026
Processing Time Days
722
Number Of Sites
1
Number Of Participants
4

Sites

Site Name
Semmelweis University
Department Name
Gyermekgyógyászati Klinika, Tűzoltó utcai részleg
Contact Person Name
Andrea Ponyi
Contact Person Email
ponyi.andrea@gyerekklinika.com

Belgium

Earliest CTIS Part Ii Submission Date
13-03-2024
Latest Decision Or Authorization Date
25-02-2026
Processing Time Days
715
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
Universitair Ziekenhuis Gent
Department Name
Pediatric Oncology
Contact Person Name
Bram De Wilde
Contact Person Email
bram.dewilde@uzgent.be

Denmark

Earliest CTIS Part Ii Submission Date
18-03-2024
Latest Decision Or Authorization Date
02-02-2026
Processing Time Days
687
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Rigshospitalet
Department Name
Klinisk Forsøgsenhed for Børn og Unge med Kræft Afdeling for Børn og Unge
Contact Person Name
Ruta Tuckuviene
Contact Person Email
ruta.tuckuviene@regionh.dk

Czechia

Earliest CTIS Part Ii Submission Date
13-03-2024
Latest Decision Or Authorization Date
24-02-2026
Processing Time Days
714
Number Of Sites
2
Number Of Participants
4

Sites

Site Name
Fakultni Nemocnice Brno
Department Name
Klinika dětské onkologie
Contact Person Name
Peter Múdry
Contact Person Email
mudry.peter@fnbrno.cz
Site Name
Fakultni Nemocnice V Motole
Department Name
Klinika dětské hematologie a onkologie
Contact Person Name
Michaela Čepelová
Contact Person Email
Michaela.Cepelova@fnmotol.cz

Greece

Earliest CTIS Part Ii Submission Date
15-03-2024
Latest Decision Or Authorization Date
02-02-2026
Processing Time Days
690
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Nosokomeio Paidon I Agia Sofia
Department Name
1st Pathology Clinic-Department of Paediatric Oncology/Heamatology
Contact Person Name
Antonios Kattamis
Contact Person Email
ankatt@med.uoa.gr

Sponsor

Primary sponsor

Full Name
Merck Sharp & Dohme LLC
Organisation Type
Pharmaceutical company
Country Of Registered Address
United States

Contract research organisations

Name
Pharmaceutical Product Development LLC
Responsibilities
code: 4
Name
Parexel International Corp.
Responsibilities
Medical information (Physician Consulting)
Name
Eresearchtechnology Inc.
Responsibilities
central imaging
Name
Almac Clinical Technologies LLC
Responsibilities
code: 3
Name
Covance Central Laboratory Services Inc.
Responsibilities
central laboratory (code: 4)
Name
Perceptive Eclinical Limited
Responsibilities
EUB Call center and medical escalation service
Name
Infinity Biologix LLC
Responsibilities
DNA extraction of buccal swabs and sample storage

Third parties

  • {"country":"United States","full_name":"Pharmaceutical Product Development LLC","duties_or_roles":"code: 4","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Parexel International Corp.","duties_or_roles":"Medical information (Physician Consulting)","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Eresearchtechnology Inc.","duties_or_roles":"central imaging","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Almac Clinical Technologies LLC","duties_or_roles":"code: 3","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Covance Central Laboratory Services Inc.","duties_or_roles":"code: 4","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Perceptive Eclinical Limited","duties_or_roles":"EUB Call center and medical escalation service","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Infinity Biologix LLC","duties_or_roles":"DNA extraction of buccal swabs and storage of samples until an anlysis lab is identified.","organisation_type":"Pharmaceutical company"}

Investigational products

Investigational Product Name
Zilovertamab vedotin
Active Substance
ZILOVERTAMAB VEDOTIN
Modality
ADC|Monoclonal antibody
Routes Of Administration
INTRAVENOUS INFUSION
Route
INTRAVENOUS INFUSION
Authorisation Status
Investigational product (IMP11011/00003)

Related trials

Other published trials that may interest you.