Clinical trial • Phase I/II • Musculoskeletal

VX-670 for Myotonic dystrophy type 1

Phase I/II trial of VX-670 for Myotonic dystrophy type 1. open-label. 20 participants.

Overview

Trial Therapeutic Area
Musculoskeletal
Trial Disease
Myotonic dystrophy type 1
Trial Stage
Phase I/II
Drug Modality
Oligonucleotide

Key dates

Initial CTIS Submission Date
11-02-2025
First CTIS Authorization Date
03-06-2025

Trial design

open-label Phase I/II trial across 6 sites in Belgium, Netherlands, Spain and others.

Open Label
Yes
Target Sample Size
20

Eligibility

Recruits 20 Vulnerable populations are not selected for this trial (isVulnerablePopulationSelected: false). Informed consent must be signed and dated by the subject; if the subject is cognitively able to provide consent but unable to write, an impartial witness may sign ("Subject (or his or her impartial witness if the subject is cognitively able to provide consent but unable to write) will sign and date an informed consent form (ICF)"). All provided ICFs and subject information documents are adult-focused and country/language-specific (multiple language versions available). No assent process for minors is specified..

Pregnancy Exclusion
3. For female subjects: Pregnant, nursing, or planning to become pregnant during the study or within 180 days after the last dose of study drug. For male subjects: Male subjects with a female partner who is pregnant, nursing, or planning to become pregnant during the study or within 180 days after the last dose of study drug.
Vulnerable Population
Vulnerable populations are not selected for this trial (isVulnerablePopulationSelected: false). Informed consent must be signed and dated by the subject; if the subject is cognitively able to provide consent but unable to write, an impartial witness may sign ("Subject (or his or her impartial witness if the subject is cognitively able to provide consent but unable to write) will sign and date an informed consent form (ICF)"). All provided ICFs and subject information documents are adult-focused and country/language-specific (multiple language versions available). No assent process for minors is specified.

Inclusion criteria

  • {"criterion_text":"- 1. Subject (or his or her impartial witness if the subject is cognitively able to provide consent but unable to write) will sign and date an informed consent form (ICF).\n- 2. Subject must have completed an interventional VX-670 study (per interventional study completion definition) a. Study 001: Subjects in Part B must have received at least 2 doses of study drug.\n- 3. Willing and able to comply with scheduled visits, treatment plan, study restrictions, safety tests, contraceptive guidelines, and other study procedures."}

Exclusion criteria

  • {"criterion_text":"- 1. History or evidence of any illness or any clinical condition (e.g. clinically significant kidney disease) that, in the opinion of the investigator or the subject’s general practitioner, might confound the results of the study or pose an additional risk in administering study drug to the subject. This may include but is not limited to major surgery, significant trauma, or clinically significant laboratory abnormalities (e.g., hypomagnesemia) within 4 weeks before the first study drug dose.\n- 2.\tSubject developed any VX-670-related serious or severe AE in the interventional study that, in the opinion of the sponsor, might pose an additional risk to the subject.\n- 3. For female subjects: Pregnant, nursing, or planning to become pregnant during the study or within 180 days after the last dose of study drug. For male subjects: Male subjects with a female partner who is pregnant, nursing, or planning to become pregnant during the study or within 180 days after the last dose of study drug.\n- 4. Use of the substances, activities, or devices as indicated in Section 9.4, during the specified times.\n- 5. Exposure to any investigational nucleic acid or cell and genetic therapy other than VX-670, including siRNA, ASO, mRNA within 6 months before Day 1 or 5 half-lives of investigational agent (confirmed at Screening), whichever is longer.\n- 6. Exposure to any cell and genetic therapies. Note that antisense oligonucleotides are not considered a genetic therapy.\n- 7. Exposure to any other investigational drugs or devices within 1 month before Day 1 or 5 half-lives before the first dose of study drug, whichever is longer\n- 8. Subject, or close relative of the subject, is the investigator or a subinvestigator, research assistant, pharmacist, study coordinator, or other staff directly involved with the conduct of the study at that site.\n- 9. Subject is an employee of the sponsor."}

Endpoints

Primary endpoints

  • {"endpoint_text":"- Safety and tolerability of VX-670 based on the assessment of adverse events (AEs), vital signs, electrocardiograms (ECGs), and clinical laboratory values","definition_or_measurement_approach":"Assessment of adverse events (AEs), vital signs, electrocardiograms (ECGs), and clinical laboratory values."}

Secondary endpoints

  • {"endpoint_text":"- VX-670 and PMO-0221a concentrations in plasma","definition_or_measurement_approach":"Measurement of plasma concentrations of VX-670 and PMO-0221a (plasma PK)."}

Recruitment

Planned Sample Size
20
Recruitment Window Months
44
Consent Approach
Informed consent is obtained from each adult subject; the subject signs and dates the informed consent form (ICF). If the subject is cognitively able to provide consent but unable to write, an impartial witness may sign the ICF on their behalf. ICFs and subject information sheets are provided in multiple language and country-specific versions (e.g., English, French, Dutch, German, Italian, Spanish) as indicated by the available country-specific L1/SIS and ICF documents.

Geography

Total Number Of Sites
6
Total Number Of Participants
20

Belgium

Earliest CTIS Part Ii Submission Date
29-04-2025
Latest Decision Or Authorization Date
01-07-2025
Processing Time Days
63
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
UZ Leuven
Department Name
Neurology
Contact Person Name
Kristl Claeys
Contact Person Email
kristl.claeys@uzleuven.be
Number Of Participants
3

Netherlands

Earliest CTIS Part Ii Submission Date
29-04-2025
Latest Decision Or Authorization Date
03-06-2025
Processing Time Days
35
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Academisch Ziekenhuis Maastricht
Department Name
Neurology, School of Mental Health and Neurosciences
Contact Person Name
Karin Faber
Contact Person Email
c.faber@mumc.nl
Number Of Participants
2

Spain

Earliest CTIS Part Ii Submission Date
23-05-2025
Latest Decision Or Authorization Date
01-07-2025
Processing Time Days
39
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Hospital Universitario Y Politecnico La Fe
Department Name
Neurología
Contact Person Name
Nuria Muelas Gómez
Contact Person Email
nuriamugo@gmail.com
Number Of Participants
2

Italy

Earliest CTIS Part Ii Submission Date
23-04-2025
Latest Decision Or Authorization Date
04-06-2025
Processing Time Days
42
Number Of Sites
1
Number Of Participants
4

Sites

Site Name
Centro Clinico Nemo
Department Name
UOC Neuroriabilitazione Neurologica
Contact Person Name
Valeria Sansone
Number Of Participants
4

France

Earliest CTIS Part Ii Submission Date
28-04-2025
Latest Decision Or Authorization Date
04-06-2025
Processing Time Days
37
Number Of Sites
1
Number Of Participants
5

Sites

Site Name
Association Institut De Myologie
Department Name
Neuromyology
Contact Person Name
Guillaume Bassez
Contact Person Email
guillaume.bassez@aphp.fr
Number Of Participants
5

Germany

Earliest CTIS Part Ii Submission Date
21-05-2025
Latest Decision Or Authorization Date
01-07-2025
Processing Time Days
41
Number Of Sites
1
Number Of Participants
4

Sites

Site Name
Friedrich Baur Institute An Der Neurologischen Klinik Und Poliklinik
Department Name
Neurologische Klinik und Poliklinik
Contact Person Name
Stephan Wenninger
Number Of Participants
4

Sponsor

Primary sponsor

Full Name
Vertex Pharmaceuticals Inc.
Organisation Type
Pharmaceutical company
Country Of Registered Address
United States

Investigational products

Investigational Product Name
VX-670 Solution for Injection/Infusion
Active Substance
VX-670
Modality
Oligonucleotide
Routes Of Administration
Intravenous administration
Route
Intravenous administration

Related trials

Other published trials that may interest you.