Clinical trial • Phase IV • Haematology

SIMOCTOCOG ALFA for Haemophilia A

Phase IV trial of SIMOCTOCOG ALFA for Haemophilia A. None/Not specified-controlled. 101 participants.

Overview

Trial Therapeutic Area
Haematology
Trial Disease
Haemophilia A
Trial Stage
Phase IV
Drug Modality
Bispecific antibody|Peptide/protein/enzyme
Paediatric Trial
Yes

Key dates

Initial CTIS Submission Date
30-07-2024
First CTIS Authorization Date
27-08-2024

Trial design

None/Not specified-controlled Phase IV trial across 14 sites in Germany, Norway, Sweden and others.

Comparator
None/Not specified
Target Sample Size
101

Eligibility

Recruits 101 paediatric patients.

Vulnerable Population
Participants may be of any age (including children). The protocol requires that participants or the participants’ parent(s)/legal guardian(s) be capable of giving signed informed consent and understanding trial documents. Age-specific assent and consent documents are provided (children assent and teenager assent forms and parent/guardian information/ICF documents are included in the submitted documentation), indicating that minors will provide assent appropriate to age bands and parents/guardians provide consent.

Inclusion criteria

  • {"criterion_text":"- 1.\tParticipants can be of any age at the time of enrolment into the trial."}
  • {"criterion_text":"- 2.\tMale persons with hemophilia A (HA), of any severity, who have a historical inhibitor titre ≥ 0.6 BU/mL, including those who have failed previous ITI attempt(s)"}
  • {"criterion_text":"- 3.\tPersons undergoing ITI with Nuwiq®, octanate® or wilate® or undergoing ITI with Nuwiq®, octanate® or wilate® and receiving prophylactic therapy with emicizumab, aPCC or rFVIIa"}
  • {"criterion_text":"- 4.\tParticipants or participants’ parent(s)/legal guardian(s) must be capable of giving signed informed consent and be able to understand the trial documents"}

Exclusion criteria

  • {"criterion_text":"- 1.\tParticipants are excluded from the trial if any coagulation disorder other than HA is diagnosed"}
  • {"criterion_text":"- 2.\tPartly retrospective patients will be excluded if detailed documentation on treatment, all BEs, inhibitor titres and FVIII levels is not available for the retrospective period"}

Endpoints

Primary endpoints

  • {"endpoint_text":"- The primary endpoint in Group 1 and Group 2 is to evaluate ITI outcome as determined by achievement of the following ITI criteria: 1.\tInhibitor titre < 0.6 BU/mL for at least 2 consecutive measurements 2.\tFVIII recovery ≥ 66% of the predefined reference value of 1.5% IU/kg BW 3.\tFVIII half-life ≥ 6 h","definition_or_measurement_approach":"Measured laboratory criteria: serial inhibitor titre measurements (Bethesda units) showing <0.6 BU/mL on at least two consecutive measurements; FVIII recovery assessed relative to predefined reference value (≥66% of 1.5% IU/kg BW); FVIII half-life measured and confirmed ≥ 6 hours."}
  • {"endpoint_text":"- The primary endpoint for Group 3 is to evaluate the ABR compared with the ABR in Group 1 and Group 2.","definition_or_measurement_approach":"Annualised bleeding rate (ABR) calculated for participants in Group 3 and compared against ABR in Groups 1 and 2 (standard ABR calculation over observation period)."}

Secondary endpoints

  • {"endpoint_text":"- For participants in Group 1 and Group 2: 1.\tTime to achieve ITI outcome 2.\tUse of emicizumab, aPCC, rFVIIa during ITI 3.\tRate of FVIII inhibitor relapses during a follow-up period in participants who have achieved complete ITI success","definition_or_measurement_approach":"Time-to-event analysis for time to achieve ITI outcome; recording and summarising use of emicizumab, aPCC and rFVIIa during ITI; tracking and reporting relapses of FVIII inhibitors during follow-up in participants who achieved complete ITI success."}
  • {"endpoint_text":"- For participants in all 3 groups: 1.\tFrequency and severity of all bleeding episodes (BEs), all treated BEs, all spontaneous BEs, all joint BEs, and target joint BEs over time (≥ 3 bleeds in the same joint within 24 weeks) 2.\tNumber of infusions required to control BEs 3.\tFrequency and severity of bleeding during and after surgical procedures","definition_or_measurement_approach":"Bleeding episodes captured and categorised (treated, spontaneous, joint, target joint); frequency and severity summarised over time; count of infusions required to control BEs and collection of bleeding events related to surgical procedures."}
  • {"endpoint_text":"- For participants in all 3 groups: 4.\tProportion of participants experiencing ADRs 5.\tThrombotic events (location, treatment, outcome) 6.\tTreatment costs","definition_or_measurement_approach":"Safety endpoints: proportion with adverse drug reactions (ADRs), documentation of thrombotic events with location/treatment/outcome; health-economic data collection for treatment costs."}

Recruitment

Planned Sample Size
101
Recruitment Window Months
110
Consent Approach
Informed consent is required from participants or, for minors, from parent(s)/legal guardian(s) (inclusion criterion: participants or participants’ parent(s)/legal guardian(s) must be capable of giving signed informed consent and understanding trial documents). Age-appropriate assent forms and parent/guardian information/ICF documents are provided (children assent and teenager assent forms and parent/guardian ICFs are included among submitted documents), indicating age-specific consent/assent handling across multiple paediatric age bands.

Geography

Total Number Of Sites
14
Total Number Of Participants
22

Germany

Earliest CTIS Part Ii Submission Date
20-08-2024
Latest Decision Or Authorization Date
11-07-2025
Processing Time Days
325
Number Of Sites
5
Number Of Participants
6

Sites

Site Name
Gerinnungszentrum Rhein-Ruhr Aerztepartnerschaft Dr. med. Hannelore Rott Fachaerztin fuer Transfusionsmedizin Haemostaseologie Dr. med. Susan Halimeh Fachaerztin fuer Transfusionsmedizin Haemostaseologie Dr. med. Guenther Kappert Facharzt fuer Laboratoriumsmedizin Haemostaseologie
Principal Investigator Name
Susan Halimeh
Principal Investigator Email
Susan.halimeh@gzrr.de
Contact Person Name
Susan Halimeh
Contact Person Email
Susan.halimeh@gzrr.de
Site Name
Universitaetsklinikum Muenster AöR
Department Name
Klinik für Kinder- und Jugendmedizin
Principal Investigator Name
Meike Nowacki
Principal Investigator Email
meike.nowacki@ukmuenster.de
Contact Person Name
Meike Nowacki
Contact Person Email
meike.nowacki@ukmuenster.de
Site Name
HZRM Haemophilie-Zentrum Rhein Main GmbH
Principal Investigator Name
Carmen Escuriola
Principal Investigator Email
carmen.escuriola@hzrm.de
Contact Person Name
Carmen Escuriola
Contact Person Email
carmen.escuriola@hzrm.de
Site Name
Justus-Liebig-Universitaet Giessen
Department Name
Sektion Haemostaseologie
Principal Investigator Name
Ulrich Sachs
Principal Investigator Email
ulrich.sachs@med.uni-giessen.de
Contact Person Name
Ulrich Sachs
Site Name
Universitaetsklinikum Bonn AöR
Department Name
Insititut für Experimentelle Haematologie und Transfusionsmedizin (IHT)
Principal Investigator Name
Johannes Oldenburg
Principal Investigator Email
johannes.oldenburg@ukbonn.de
Contact Person Name
Johannes Oldenburg
Contact Person Email
johannes.oldenburg@ukbonn.de

Norway

Earliest CTIS Part Ii Submission Date
20-08-2024
Latest Decision Or Authorization Date
09-07-2025
Processing Time Days
323
Number Of Sites
1
Number Of Participants
5

Sites

Site Name
Oslo University Hospital HF
Department Name
Center for rare diagnostics
Principal Investigator Name
Heidi Glosli
Principal Investigator Email
hglosli@ous-hf.no
Contact Person Name
Heidi Glosli
Contact Person Email
hglosli@ous-hf.no

Sweden

Earliest CTIS Part Ii Submission Date
20-08-2024
Latest Decision Or Authorization Date
08-07-2025
Processing Time Days
322
Number Of Sites
1
Number Of Participants
2

Sites

Site Name
Region Skane Skanes Universitetssjukhus
Department Name
Department of hematology
Principal Investigator Name
Jan Astermark
Principal Investigator Email
Jan.Astermark@med.lu.se
Contact Person Name
Jan Astermark
Contact Person Email
Jan.Astermark@med.lu.se

Finland

Earliest CTIS Part Ii Submission Date
20-08-2024
Latest Decision Or Authorization Date
08-07-2025
Processing Time Days
322
Number Of Sites
1
Number Of Participants
1

Sites

Site Name
HUS-Yhtymae
Department Name
New Children’s Hospital
Principal Investigator Name
Satu Långström
Principal Investigator Email
satu.langstrom@hus.fi
Contact Person Name
Satu Långström
Contact Person Email
satu.langstrom@hus.fi

Croatia

Earliest CTIS Part Ii Submission Date
20-08-2024
Latest Decision Or Authorization Date
21-07-2025
Processing Time Days
335
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
University Hospital Centre Zagreb
Department Name
Internal medicine
Principal Investigator Name
Ana Boban
Principal Investigator Email
ana.boban@kbc-zagreb.hr
Contact Person Name
Ana Boban
Contact Person Email
ana.boban@kbc-zagreb.hr

Spain

Earliest CTIS Part Ii Submission Date
20-08-2024
Latest Decision Or Authorization Date
29-08-2025
Processing Time Days
374
Number Of Sites
4
Number Of Participants
2

Sites

Site Name
Hospital Universitari Vall D Hebron
Department Name
Dept of Hematology and Hemotherapy
Principal Investigator Name
Olga Benitez Hidalgo
Principal Investigator Email
obenitez@vhebron.net
Contact Person Name
Olga Benitez Hidalgo
Contact Person Email
obenitez@vhebron.net
Site Name
University Hospital Virgen Del Rocio S.L.
Department Name
Hematology Department
Principal Investigator Name
Ramiro Nuñez Vazquez
Principal Investigator Email
ramirojosenv@gmail.com
Contact Person Name
Ramiro Nuñez Vazquez
Contact Person Email
ramirojosenv@gmail.com
Site Name
Hospital General Universitario Dr. Balmis
Department Name
Dept of Haemostasis and Thrombosis
Principal Investigator Name
Ana Marco Rico
Principal Investigator Email
marco_anaric@gva.es
Contact Person Name
Ana Marco Rico
Contact Person Email
marco_anaric@gva.es
Site Name
Hospital Universitario San Juan De Alicante
Department Name
Hematology Department
Principal Investigator Name
Ana Marco Rico
Principal Investigator Email
marco_anaric@gva.es
Contact Person Name
Ana Marco Rico
Contact Person Email
marco_anaric@gva.es

Bulgaria

Earliest CTIS Part Ii Submission Date
14-10-2025
Latest Decision Or Authorization Date
28-10-2025
Processing Time Days
14
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
Specialized Hospital For Active Treatment Of Hematological Diseases EAD
Department Name
Clinic of Pediatric Hematology for treatment of children with benign hematological diseases 0-18y
Principal Investigator Name
Atanas Banchev
Principal Investigator Email
bantschev@gmail.com
Contact Person Name
Atanas Banchev
Contact Person Email
bantschev@gmail.com

Sponsor

Primary sponsor

Full Name
HZRM Haemophilie-Zentrum Rhein Main GmbH
Organisation Type
Hospital/Clinic/Other health care facility
Country Of Registered Address
Germany

Contract research organisations

Name
Allucent (UK) Limited
Responsibilities
CRO responsibilities

Third parties

  • {"country":"United Kingdom","full_name":"Allucent (UK) Limited","duties_or_roles":"CRO responsibilities","organisation_type":"Pharmaceutical company"}
  • {"country":"Switzerland","full_name":"Universitaetsklinik Balgrist","duties_or_roles":"","organisation_type":"Hospital/Clinic/Other health care facility"}
  • {"country":"Germany","full_name":"Universitaetsklinikum Bonn AöR","duties_or_roles":"F8 mutations, FVIII inhibitor epitope mapping, Thrombotic risk markers, antiemicizumab antib detection","organisation_type":"Hospital/Clinic/Other health care facility"}
  • {"country":"Germany","full_name":"LKF Laboratorium fuer Klinische Forschung GmbH","duties_or_roles":"Coordinates laboratory samples collection and distribution","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"Switzerland","full_name":"nspm AG","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Emory Children Center","duties_or_roles":"epitope mapping","organisation_type":"Hospital/Clinic/Other health care facility"}
  • {"country":"Germany","full_name":"HZRM Haemophilie-Zentrum Rhein Main GmbH","duties_or_roles":"","organisation_type":"Hospital/Clinic/Other health care facility"}
  • {"country":"France","full_name":"Hospices Civils De Lyon","duties_or_roles":"TGA analysis","organisation_type":"Hospital/Clinic/Other health care facility"}
  • {"country":"United States","full_name":"Medidata Solutions Inc.","duties_or_roles":"","organisation_type":"Non-Pharmaceutical company"}

Co-sponsors

  • Emory University

Investigational products

Investigational Product Name
Nuwiq 250 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 500 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 1000 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 1500 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 2000 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 2500 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 3000 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Nuwiq 4000 IU powder and solvent for solution for injection
Active Substance
SIMOCTOCOG ALFA
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Octanate 250 Pulver und Lösungsmittel zur Herstellung einer Injektionslösung
Active Substance
HUMAN COAGULATION FACTOR VIII
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Octanate 500 Pulver und Lösungsmittel zur Herstellung einer Injektionslösung
Active Substance
HUMAN COAGULATION FACTOR VIII
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Octanate 1000 Pulver und Lösungsmittel zur Herstellung einer Injektionslösung
Active Substance
HUMAN COAGULATION FACTOR VIII
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Wilate 500, 500 I.E. VWF/500 I.E. FVIII, Pulver und Lösungsmittel zur Herstellung einer intravenösen Injektionslösung.
Active Substance
HUMAN COAGULATION FACTOR VIII, HUMAN VON WILLEBRAND FACTOR
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Wilate 1000, 1000 I.E. VWF/1000 I.E. FVIII, Pulver und Lösungsmittel zur Herstellung einer intravenösen Injektionslösung.
Active Substance
HUMAN COAGULATION FACTOR VIII, HUMAN VON WILLEBRAND FACTOR
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
FEIBA 2500 E Pulver und Lösungsmittel zur Herstellung einer Infusionslösung.
Active Substance
FACTOR VIII INHIBITOR BYPASSING FRACTION
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
FEIBA 500 E Pulver und Lösungsmittel zur Herstellung einer Infusionslösung.
Active Substance
FACTOR VIII INHIBITOR BYPASSING FRACTION
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
FEIBA 1000 E Pulver und Lösungsmittel zur Herstellung einer Infusionslösung
Active Substance
FACTOR VIII INHIBITOR BYPASSING FRACTION
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
Hemlibra 150 mg/mL solution for injection
Active Substance
EMICIZUMAB
Modality
Bispecific antibody
Routes Of Administration
SUBCUTANEOUS USE
Route
SUBCUTANEOUS
Authorisation Status
Authorised
Investigational Product Name
Hemlibra 30 mg/mL solution for injection
Active Substance
EMICIZUMAB
Modality
Bispecific antibody
Routes Of Administration
SUBCUTANEOUS USE
Route
SUBCUTANEOUS
Authorisation Status
Authorised
Investigational Product Name
NovoSeven 1 mg (50 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG ALFA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
NovoSeven 2 mg (100 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG ALFA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
NovoSeven 5 mg (250 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG ALFA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
NovoSeven 8 mg (400 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG ALFA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
CEVENFACTA 5 mg (225 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG BETA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
CEVENFACTA 2 mg (90 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG BETA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Investigational Product Name
CEVENFACTA 1 mg (45 KIU) powder and solvent for solution for injection
Active Substance
EPTACOG BETA (ACTIVATED)
Modality
Peptide/protein/enzyme
Routes Of Administration
INTRAVENOUS
Route
INTRAVENOUS
Authorisation Status
Authorised
Combination Treatment
Yes

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