Clinical trial • Phase III • Haematology|Immunology

ETOPOSIDE for Hemophagocytic lymphohistiocytosis

Phase III trial of ETOPOSIDE for Hemophagocytic lymphohistiocytosis.

Overview

Trial Therapeutic Area
Haematology|Immunology
Trial Disease
Hemophagocytic lymphohistiocytosis
Trial Stage
Phase III
Drug Modality
Small molecule

Key dates

Initial CTIS Submission Date
25-10-2024
First CTIS Authorization Date
10-03-2025

Trial design

Randomised, two randomized strategies: an early strategy where etoposide is initiated within 12 hours after inclusion; a delayed (expectant) strategy where etoposide is initiated only in case of unfavorable evolution after 48 hours (use of rescue etoposide in the delayed arm is considered an event). no dose or schedule for the comparator beyond timing is specified in the ctis record.-controlled Phase III trial in France.

Randomised
Yes
Comparator
Two randomized strategies: an early strategy where etoposide is initiated within 12 hours after inclusion; a delayed (expectant) strategy where etoposide is initiated only in case of unfavorable evolution after 48 hours (use of rescue etoposide in the delayed arm is considered an event). No dose or schedule for the comparator beyond timing is specified in the CTIS record.
Target Sample Size
130
Trial Duration For Participant
60

Eligibility

Recruits 130 Only adult patients are eligible; minors are explicitly excluded. Patients under legal guardianship, tutelage, or curatorship are excluded. Informed consent is obtained from the adult patient. Subject information and informed consent forms exist for adult patients and for legal representatives (documents: L1_SIS and ICF_adult patient; L1_SIS and ICF_legal representative). The trial does not select a vulnerable population in the CTIS metadata (isVulnerablePopulationSelected: false)..

Pregnancy Exclusion
Pregnant or lactating woman
Vulnerable Population
Only adult patients are eligible; minors are explicitly excluded. Patients under legal guardianship, tutelage, or curatorship are excluded. Informed consent is obtained from the adult patient. Subject information and informed consent forms exist for adult patients and for legal representatives (documents: L1_SIS and ICF_adult patient; L1_SIS and ICF_legal representative). The trial does not select a vulnerable population in the CTIS metadata (isVulnerablePopulationSelected: false).

Inclusion criteria

  • {"criterion_text":"- Adult patient\n- Confirmed diagnosis of HLH: • Presence of 5 or more Henter criteria (HLH-04) out of the 6 achievable in routine care (fever, splenomegaly, cytopenias affecting 2 or 3 blood lineages, hypertriglyceridemia or hypofibrinogenemia, hemophagocytosis in bone marrow, spleen or lymph nodes, hyperferritinemia) • Diagnosis of HLH established by the multidisciplinary team caring for the patient\n- First episode of HLH\n- Admission to intensive care unit\n- Presence of one or more organ failures • Circulatory: mBP < 65 mmHg with lactate > 2 mmol/L, or treatment with catecholamines • Respiratory: oxygen therapy > 6L/min or need for non-invasive ventilation, high-flow nasal cannula oxygen therapy, or invasive mechanical ventilation • Renal: stage 2 or higher according to KDIGO criteria, either creatinine 2-2.9 times baseline, or urine output < 0.5 mL/kg/h for 12 hours • Neurological: GCS ≤ 13"}

Exclusion criteria

  • {"criterion_text":"- Moribund patient with refractory distributive shock: multi-organ failure requiring noradrenaline >2.5 μg/kg/min and imminent risk of death\n- Participation in another interventional research study\n- Inability to administer etoposide within 12 hours\n- Patient treated with etoposide prior to admission to the intensive care unit\n- Hypersensitivity to etoposide or any of its excipients\n- Patient not covered by social security\n- Patient under legal guardianship, tutelage, or curatorship\n- Minor patient\n- Pregnant or lactating woman\n- Recent vaccination with a live attenuated vaccine"}

Endpoints

Primary endpoints

  • {"endpoint_text":"- The occurrence of an event defined as the onset or worsening of organ failures, evaluated using the modified Sequential Organ Failure Assessment (SOFA) score (excluding the hematologic component). An event will be defined as an increase of at least 1 point for at least two organ systems compared to Day 0. In the delayed arm, the use of rescue etoposide treatment or in case of secondary aggravation during follow-up will also be considered an event.","definition_or_measurement_approach":"Evaluated using the modified SOFA score excluding hematologic component; event = increase ≥1 point in at least two organ systems vs Day 0. In delayed arm, initiation of rescue etoposide or secondary aggravation during follow-up is also counted as an event."}

Secondary endpoints

  • {"endpoint_text":"- Time to death after inclusion (with a maximum follow-up duration of 60 days)\n- Number of ventilator-free days between inclusion and Day 14\n- Number of catecholamine-free days between inclusion and Day 14\n- Proportion of patients receiving at least one session of renal replacement therapy between inclusion and Day 14\n- Length of stay in the intensive care unit\n- Length of hospital stay\n- Proportion of patients receiving a dose of etoposide\n- Cumulative dose of etoposide over the first 14 days, within the total study population and among those receiving at least one dose of treatment\n- Number of days between inclusion and initiation of etoposide treatment\n- Number of patients receiving another immunosuppressive treatment during the intensive care unit stay up to Day 14\n- Time from inclusion to normalization of fibrinogen (> 2 g/L), decrease in ferritin (< 2000 μg/L), and decrease in triglycerides (< 1.5 mg/dL) during the intensive care unit stay up to Day 14\n- HScore at Days 2, 7, and 14\n- Proportion of patients experiencing healthcare-associated infections, acquired neutropenia after inclusion (defined by ANC < 500/mm³) and its duration if applicable, and post-inclusion bleeding event requiring transfusion and/or surgical intervention\n- Delta SOFA at Days 2 and 5, maximum SOFA score, including both SOFA and modified SOFA","definition_or_measurement_approach":"Time to death: measured from inclusion up to maximum follow-up of 60 days. Ventilator-/catecholamine-free days: counted between inclusion and Day 14. Renal replacement therapy: proportion receiving ≥1 session between inclusion and Day 14. Cumulative etoposide dose: total over first 14 days (overall and among those treated). Time to initiation: days from inclusion to first etoposide. Other laboratory endpoints: fibrinogen >2 g/L, ferritin <2000 μg/L, triglycerides <1.5 mg/dL measured during ICU stay up to Day14. HScore assessed at Days 2,7,14. Neutropenia defined as ANC <500/mm3. SOFA endpoints: delta SOFA at Days 2 and 5 and maximum SOFA including modified SOFA."}

Recruitment

Planned Sample Size
130
Recruitment Window Months
36
Consent Approach
Informed consent is obtained from the adult patient. Subject information and informed consent forms exist for adult patients and for legal representatives (documents listed: L1_SIS and ICF_adult patient; L1_SIS and ICF_legal representative; and pursuit versions). Minors are excluded; patients under legal guardianship/tutelage/curatorship are excluded. Languages of the consent documents are not specified in the CTIS metadata.

Geography

Total Number Of Sites
27
Total Number Of Participants
130

France

Earliest CTIS Part Ii Submission Date
05-12-2024
Latest Decision Or Authorization Date
10-03-2025
Processing Time Days
95
Number Of Sites
27
Number Of Participants
130

Sites

Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Bruno Mégarbane
Principal Investigator Email
guillaume.chevrel@chsf.fr
Contact Person Name
Bruno Mégarbane
Contact Person Email
guillaume.chevrel@chsf.fr
Site Name
Centre Hospitalier De Versailles
Department Name
Intensive Care Unit
Principal Investigator Name
Stéphane Legriel
Principal Investigator Email
slegriel@ght78sud.fr
Contact Person Name
Stéphane Legriel
Contact Person Email
slegriel@ght78sud.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Etienne De Montmollin
Principal Investigator Email
Etienne.demontmollin@aphp.fr
Contact Person Name
Etienne De Montmollin
Contact Person Email
Etienne.demontmollin@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Nicholas Heming
Principal Investigator Email
nicholas.heming@aphp.fr
Contact Person Name
Nicholas Heming
Contact Person Email
nicholas.heming@aphp.fr
Site Name
CHRU De Nancy
Department Name
Intensive Care Unit
Principal Investigator Name
Pierre Perez
Principal Investigator Email
p.perez@chru-nancy.fr
Contact Person Name
Pierre Perez
Contact Person Email
p.perez@chru-nancy.fr
Site Name
Centre Hospitalier Sud Francilien
Department Name
Intensive Care Unit
Principal Investigator Name
Guillaume Chevrel
Principal Investigator Email
guillaume.chevrel@chsf.fr
Contact Person Name
Guillaume Chevrel
Contact Person Email
guillaume.chevrel@chsf.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Fabrice Uhel
Principal Investigator Email
fabrice.uhel@aphp.fr
Contact Person Name
Fabrice Uhel
Contact Person Email
fabrice.uhel@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Jean-Luc Diehl
Principal Investigator Email
jean-luc.diehl@aphp.fr
Contact Person Name
Jean-Luc Diehl
Contact Person Email
jean-luc.diehl@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Frédéric Pène
Principal Investigator Email
Frederic.pene@aphp.fr
Contact Person Name
Frédéric Pène
Contact Person Email
Frederic.pene@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Nicolas De Prost
Principal Investigator Email
Nicolas.de-prost@aphp.fr
Contact Person Name
Nicolas De Prost
Contact Person Email
Nicolas.de-prost@aphp.fr
Site Name
Centre Hospitalier Universitaire De Montpellier
Department Name
Intensive Care Unit
Principal Investigator Name
Kada Klouche
Principal Investigator Email
k-klouche@chu-montpellier.fr
Contact Person Name
Kada Klouche
Contact Person Email
k-klouche@chu-montpellier.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Olivier Roux
Principal Investigator Email
olivier.roux@aphp.fr
Contact Person Name
Olivier Roux
Contact Person Email
olivier.roux@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Eric Maury
Principal Investigator Email
eric.maury@aphp.fr
Contact Person Name
Eric Maury
Contact Person Email
eric.maury@aphp.fr
Site Name
Centre Hospitalier Victor Dupouy
Department Name
Intensive Care Unit
Principal Investigator Name
Damien Contou
Principal Investigator Email
damien.contou@ch-argenteuil.fr
Contact Person Name
Damien Contou
Contact Person Email
damien.contou@ch-argenteuil.fr
Site Name
Centre Hospitalier Universitaire De Dijon
Department Name
Intensive Care Unit
Principal Investigator Name
Jean-Pierre Quenot
Principal Investigator Email
jean-pierre.quenot@chu-dijon.fr
Contact Person Name
Jean-Pierre Quenot
Site Name
Centre Hospitalier Universitaire D Orleans
Department Name
Intensive Care Unit
Principal Investigator Name
François Barbier
Principal Investigator Email
francois.barbier@chr-orleans.fr
Contact Person Name
François Barbier
Site Name
Centre Hospitalier Regional De Marseille
Department Name
Intensive Care Unit
Principal Investigator Name
Sami Hraiech
Principal Investigator Email
Sami.hraiech@ap-hm.fr
Contact Person Name
Sami Hraiech
Contact Person Email
Sami.hraiech@ap-hm.fr
Site Name
Centre Hospitalier Universitaire de la Guadeloupe
Department Name
Intensive Care Unit
Principal Investigator Name
Frédéric Martino
Principal Investigator Email
frederic.martino@chu-guadeloupe.fr
Contact Person Name
Frédéric Martino
Site Name
Centre Hospitalier Universitaire Rouen
Department Name
Intensive Care Unit
Principal Investigator Name
Maximilien Grall
Principal Investigator Email
maximilien.Grall@chu-rouen.fr
Contact Person Name
Maximilien Grall
Contact Person Email
maximilien.Grall@chu-rouen.fr
Site Name
Centre Hospitalier Universitaire Amiens Picardie
Department Name
Intensive Care Unit
Principal Investigator Name
Yoann Zerbib
Principal Investigator Email
Zerbib.yoann@chu-amiens.fr
Contact Person Name
Yoann Zerbib
Contact Person Email
Zerbib.yoann@chu-amiens.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Adrien Joseph
Principal Investigator Email
adrien.joseph@aphp.fr
Contact Person Name
Adrien Joseph
Contact Person Email
adrien.joseph@aphp.fr
Site Name
Centre Hospitalier Universitaire De Lille
Department Name
Intensive Care Unit
Principal Investigator Name
Anne-Sophie Moreau
Principal Investigator Email
Annesophie.MOREAU@chu-lille.fr
Contact Person Name
Anne-Sophie Moreau
Contact Person Email
Annesophie.MOREAU@chu-lille.fr
Site Name
Centre Hospitalier Universitaire De Nice
Department Name
Intensive Care Unit
Principal Investigator Name
Mathieu Joswiak
Principal Investigator Email
jozwiak.m@chu-nice.fr
Contact Person Name
Mathieu Joswiak
Contact Person Email
jozwiak.m@chu-nice.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Julien Schmidt
Principal Investigator Email
julien.schmidt@aphp.fr
Contact Person Name
Julien Schmidt
Contact Person Email
julien.schmidt@aphp.fr
Site Name
Centre Hospital Region Metz Thionville
Department Name
Intensive Care Unit
Principal Investigator Name
Guillaume Louis
Principal Investigator Email
guillaume.louis@chr-metz-thionville.fr
Contact Person Name
Guillaume Louis
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Guillaume Voiriot
Principal Investigator Email
Guillaume.voiriot@aphp.fr
Contact Person Name
Guillaume Voiriot
Contact Person Email
Guillaume.voiriot@aphp.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Intensive Care Unit
Principal Investigator Name
Tai Pham
Principal Investigator Email
Tai.pham@aphp.fr
Contact Person Name
Tai Pham
Contact Person Email
Tai.pham@aphp.fr

Sponsor

Primary sponsor

Full Name
Assistance Publique Hopitaux De Paris
Organisation Type
Hospital/Clinic/Other health care facility
Country Of Registered Address
France

Investigational products

Investigational Product Name
ETOPOSIDE
Active Substance
ETOPOSIDE
Modality
Small molecule
Routes Of Administration
IV INJECTION, IV INFUSION
Route
IV INJECTION, IV INFUSION
Maximum Dose
100 mg/m2 daily; max total 450 mg

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