Clinical trial • Phase III • Haematology

CROVALIMAB for Paroxysmal nocturnal hemoglobinuria

Phase III trial of CROVALIMAB for Paroxysmal nocturnal hemoglobinuria.

Overview

Trial Therapeutic Area
Haematology
Trial Disease
Paroxysmal nocturnal hemoglobinuria
Trial Stage
Phase III
Drug Modality
Monoclonal antibody
Paediatric Trial
Yes

Key dates

Initial CTIS Submission Date
21-05-2024
First CTIS Authorization Date
28-06-2024

Trial design

Randomised, open-label, eculizumab (eculizumab) - concentrate for solution for infusion; active substance eculizumab; intravenous route; product data lists max daily dose amount 900 mg (dosing schedule not specified in ctis json).-controlled Phase III trial in Sweden, France, Lithuania and others.

Randomised
Yes
Open Label
Yes
Comparator
Eculizumab (ECULIZUMAB) - concentrate for solution for infusion; active substance ECULIZUMAB; intravenous route; product data lists max daily dose amount 900 mg (dosing schedule not specified in CTIS JSON).
Target Sample Size
167
Trial Duration For Participant
284

Eligibility

Recruits 167 paediatric patients.

Vulnerable Population
Vulnerable population selected. The trial includes adolescents and pediatric patients (documents and ICFs provided for minors). Assent and parental/guardian consent processes are used: parental/parental ICFs and infant authorization forms are provided; assent forms exist for age groups (e.g. 7-11 years, 12-14/12-16 years, 15-17 years). Country-specific subject information and ICF documents are provided in multiple languages (versions for EN, FR, ES, PT, NL, PL, LT, SE, RO, DE appear among submitted ICFs).

Inclusion criteria

  • {"criterion_text":"- Body weight ≥ 40 kg (pediatric patients with body weight < 40 kg)\n- Documented diagnosis of PNH, confirmed by high sensitivity flow cytometry evaluation of WBCs\n- LDH level ≥2 x ULN at screening (as per local assessment)\n- Platelet count >= 30,000/mm*3 at screening without transfusion support within 7 days of lab testing\n- ANC > 500/micro L at screening\n- For female patients of childbearing potential: agreement to remain abstinent or use contraception"}

Exclusion criteria

  • {"criterion_text":"- Current or previous treatment with a complement inhibitor\n- History of allogeneic bone marrow transplantation\n- History of Neisseria meningitidis infection within 6 months prior to screening and up to first study drug administration\n- History of myelodysplastic syndrome with Revised International Prognostic Scoring System (IPSS-R) prognostic risk categories of intermediate, high and very high\n- Splenectomy <= 6 months prior to screening\n- History of or ongoing cryoglobulinemia at screening"}

Endpoints

Primary endpoints

  • {"endpoint_text":"- 1. Proportion of patients who achieve transfusion avoidance","definition_or_measurement_approach":"Proportion of patients meeting the criterion of transfusion avoidance (binary outcome assessed per patient during the relevant evaluation period)."}
  • {"endpoint_text":"- 2. Proportion of patients with hemolysis control, measured by LDH <=1.5×ULN","definition_or_measurement_approach":"Proportion of patients with lactate dehydrogenase (LDH) ≤ 1.5 × upper limit of normal (ULN) (LDH measured by local assessment)."}

Secondary endpoints

  • {"endpoint_text":"- 1. Proportion of patients with breakthrough hemolysis","definition_or_measurement_approach":"Proportion of patients experiencing breakthrough hemolysis (as defined in protocol; no additional detail in CTIS JSON)."}
  • {"endpoint_text":"- 2. Proportion of patients with stabilization of hemoglobin","definition_or_measurement_approach":"Proportion of patients achieving haemoglobin stabilization (exact protocol definition not included in JSON)."}
  • {"endpoint_text":"- 3. Mean change in fatigue, as assessed by the Functional Assessment of Chronic Illness Therapy (FACIT)-Fatigue","definition_or_measurement_approach":"Mean change from baseline in FACIT-Fatigue score (instrument: FACIT-Fatigue)."}
  • {"endpoint_text":"- 4. Incidence and severity of adverse events","definition_or_measurement_approach":"Incidence and severity graded by standard AE reporting (no additional definition in JSON)."}
  • {"endpoint_text":"- 5. Change from baseline in targeted vital signs","definition_or_measurement_approach":"Change from baseline in pre-specified vital signs (details not provided in JSON)."}
  • {"endpoint_text":"- 6. Change from baseline in targeted clinical laboratory test results","definition_or_measurement_approach":"Change from baseline in specified clinical laboratory parameters (details not provided in JSON)."}
  • {"endpoint_text":"- 7. Incidence and severity of injection-site reactions, infusion-related reactions, hypersensitivity, and infections","definition_or_measurement_approach":"Incidence and severity of listed event types (standard AE reporting)."}
  • {"endpoint_text":"- 8. Incidence of adverse events leading to study drug discontinuation","definition_or_measurement_approach":"Incidence of AEs that result in permanent discontinuation of study drug (per investigator assessment/reporting)."}
  • {"endpoint_text":"- 9. Incidence and severity of clinical manifestations of drug-target-drug complex formation in patients who switched to crovalimab treatment from eculizumab treatment","definition_or_measurement_approach":"Incidence and severity of clinical manifestations attributed to drug-target-drug complex formation in switch patients (protocol-defined assessments; not detailed in JSON)."}
  • {"endpoint_text":"- 10. Serum concentration of crovalimab and eculizumab","definition_or_measurement_approach":"Measured serum concentrations of crovalimab and eculizumab (PK assays)."}
  • {"endpoint_text":"- 11. Prevalence and incidence of anti-drug antibodies (ADAs) to crovalimab","definition_or_measurement_approach":"Assessment of presence and incidence of anti-drug antibodies (ADA assays)."}
  • {"endpoint_text":"- 12. Change over time in pharmacodynamic biomarkers","definition_or_measurement_approach":"Longitudinal assessment of predefined pharmacodynamic biomarkers (details not provided in JSON)."}
  • {"endpoint_text":"- 13. Change over time in free C5 concentration in crovalimab-treated patients","definition_or_measurement_approach":"Longitudinal measurement of free C5 concentration in serum in crovalimab-treated participants."}
  • {"endpoint_text":"- 14. Observed value and absolute change from baseline to week 25 in parameters reflecting hemolysis","definition_or_measurement_approach":"Observed values and absolute change from baseline to Week 25 for hemolysis-related parameters (e.g., LDH and related labs; specific parameters not listed in JSON)."}

Recruitment

Registry Or Advocacy Recruitment
True, Europese Organisatie Voor Onderzoek En Behandeling Van Kanker Organisation Europeenne Pour La Recherche Et Le Traitement Du Cancer European Organi (listed as a third-party patient organisation/association)
Planned Sample Size
167
Recruitment Window Months
94
Consent Approach
Informed consent obtained from adult participants. For minors/adolescents, parental/guardian consent is used together with age-appropriate assent/infant authorization forms. Multiple country-specific ICFs and assent/parental/infant authorization documents submitted (examples: Parental ICF, Assent ICF 7-11 yrs, Assent ICF 12-14/12-16 yrs, Assent 15-17 yrs, Infant Authorization Form). Documents available in multiple language versions across countries (EN, FR, ES, PT, NL, PL, LT, SE, RO, DE as evidenced by submitted ICFs).

Geography

Total Number Of Sites
22
Total Number Of Participants
42

Sweden

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
28-06-2024
Processing Time Days
16
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
Uppsala University Hospital
Department Name
Dept. of Hematology
Principal Investigator Name
Martin Hoglund
Principal Investigator Email
martin.hoglund@medsci.uu.se
Contact Person Name
Martin Hoglund
Contact Person Email
martin.hoglund@medsci.uu.se

France

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
28-06-2024
Processing Time Days
16
Number Of Sites
2
Number Of Participants
2

Sites

Site Name
Centre Hospitalier Universitaire De Lille
Department Name
Blood Disorders
Principal Investigator Name
Louis TERRIOU
Principal Investigator Email
louis.terriou@chru-lille.fr
Contact Person Name
Louis TERRIOU
Contact Person Email
louis.terriou@chru-lille.fr
Site Name
Hospices Civils De Lyon
Department Name
Hematology
Principal Investigator Name
Fiorenza BARRACO
Principal Investigator Email
fiorenza.barraco@chu-lyon.fr
Contact Person Name
Fiorenza BARRACO
Contact Person Email
fiorenza.barraco@chu-lyon.fr

Lithuania

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
23-07-2024
Processing Time Days
41
Number Of Sites
1
Number Of Participants
1

Sites

Site Name
Vilniaus Universiteto Ligonine Santaros Klinikos Vsi
Department Name
Hematology, Oncology and Transfusion Medicine Center
Principal Investigator Name
Andrius Degulys
Principal Investigator Email
Andrius.Degulys@santa.lt
Contact Person Name
Andrius Degulys
Contact Person Email
Andrius.Degulys@santa.lt

Netherlands

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
28-06-2024
Processing Time Days
16
Number Of Sites
1
Number Of Participants
1

Sites

Site Name
Academic Medical Center at the University of Amsterdam
Department Name
Dept Hematology
Principal Investigator Name
Erfan Nur
Principal Investigator Email
e.nur@amsterdamumc.nl
Contact Person Name
Erfan Nur
Contact Person Email
e.nur@amsterdamumc.nl

Portugal

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
08-07-2024
Processing Time Days
26
Number Of Sites
3
Number Of Participants
5

Sites

Site Name
Instituto Portugues De Oncologia De Lisboa Francisco Gentil E.P.E.
Department Name
Serviço Hematologia e Oncologia Médica
Principal Investigator Name
Albertina Nunes
Principal Investigator Email
alnunes@ipolisboa.min-saude.pt
Contact Person Name
Albertina Nunes
Contact Person Email
alnunes@ipolisboa.min-saude.pt
Site Name
Unidade Local De Saude De Santo Antonio E.P.E.
Department Name
Serviço de Hematologia Clínica
Principal Investigator Name
Patrícia Seabra
Contact Person Name
Patrícia Seabra
Site Name
Unidade Local De Saude Da Regiao De Aveiro E.P.E.
Department Name
Serviço de Hematologia
Principal Investigator Name
Fernando Silva
Principal Investigator Email
Fernando.Silva.70836@chbv.min-saude.pt
Contact Person Name
Fernando Silva

Romania

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
01-07-2024
Processing Time Days
19
Number Of Sites
1
Number Of Participants
3

Sites

Site Name
Spitalul Universitar De Urgenta Bucuresti
Department Name
Sectia Hematologie
Principal Investigator Name
Ana Maria Vladareanu
Principal Investigator Email
anamariavladareanu@yahoo.com
Contact Person Name
Ana Maria Vladareanu
Contact Person Email
anamariavladareanu@yahoo.com

Poland

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
23-07-2024
Processing Time Days
41
Number Of Sites
3
Number Of Participants
7

Sites

Site Name
Mtz Clinical Research Powered By Pratia
Principal Investigator Name
Joanna Drozd-Sokołowska
Principal Investigator Email
badacz@pratia.com
Contact Person Name
Joanna Drozd-Sokołowska
Contact Person Email
badacz@pratia.com
Site Name
Uniwersytecki Szpital Kliniczny Nr 1 W Lublinie
Department Name
Klinika Hematoonkologii i Transplantacji Szpiku
Principal Investigator Name
Justyna Kozińska
Principal Investigator Email
justynakozinska@vp.pl
Contact Person Name
Justyna Kozińska
Contact Person Email
justynakozinska@vp.pl
Site Name
Uniwersyteckie Centrum Kliniczne
Department Name
Klinika Hematologii i Transplantologii
Principal Investigator Name
Agnieszka Piekarska
Principal Investigator Email
babajaga@gumed.edu.pl
Contact Person Name
Agnieszka Piekarska
Contact Person Email
babajaga@gumed.edu.pl

Spain

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
01-07-2024
Processing Time Days
19
Number Of Sites
8
Number Of Participants
12

Sites

Site Name
El Hospital Universitario De Gran Canaria Dr. Negrin
Department Name
Hematology
Principal Investigator Name
Silvia Narcisa de la Iglesia Iñigo
Principal Investigator Email
siglini@gmail.com
Contact Person Name
Silvia Narcisa de la Iglesia Iñigo
Contact Person Email
siglini@gmail.com
Site Name
Hospital General Universitario Gregorio Maranon
Department Name
Hematology
Principal Investigator Name
Monica Ballesteros Andres
Principal Investigator Email
monicabandres@hotmail.com
Contact Person Name
Monica Ballesteros Andres
Contact Person Email
monicabandres@hotmail.com
Site Name
Hospital San Pedro De Alcantara
Department Name
Hematology
Principal Investigator Name
Juan Miguel Bergua Burgues
Principal Investigator Email
jmberguaburg@gmail.com
Contact Person Name
Juan Miguel Bergua Burgues
Contact Person Email
jmberguaburg@gmail.com
Site Name
Hospital Clinico San Carlos
Department Name
Hematology
Principal Investigator Name
Fernando Ataulfo Gonzalez Fernandez
Principal Investigator Email
fernandoataulfo.gonzalez@salud.madrid.org
Contact Person Name
Fernando Ataulfo Gonzalez Fernandez
Site Name
Hospital Universitario La Paz
Department Name
Hematology
Principal Investigator Name
Marta Morado Arias
Principal Investigator Email
mmorado.hulp@salud.madrid.org
Contact Person Name
Marta Morado Arias
Contact Person Email
mmorado.hulp@salud.madrid.org
Site Name
Hospital Clinic De Barcelona
Department Name
Hematology
Principal Investigator Name
Anna Gaya Valls
Principal Investigator Email
agayav@clinic.cat
Contact Person Name
Anna Gaya Valls
Contact Person Email
agayav@clinic.cat
Site Name
Hospital Germans Trias I Pujol
Department Name
Hematology
Principal Investigator Name
Ines Hernandez Rodriguez
Principal Investigator Email
ihernandez@iconcologia.net
Contact Person Name
Ines Hernandez Rodriguez
Contact Person Email
ihernandez@iconcologia.net
Site Name
Hospital Universitario Basurto
Department Name
Hematology
Principal Investigator Name
Cristina de Barrenetxea Lekue
Principal Investigator Email
cristina.barrene@gmail.com
Contact Person Name
Cristina de Barrenetxea Lekue
Contact Person Email
cristina.barrene@gmail.com

Germany

Earliest CTIS Part Ii Submission Date
12-06-2024
Latest Decision Or Authorization Date
28-06-2024
Processing Time Days
16
Number Of Sites
2
Number Of Participants
8

Sites

Site Name
Universitaetsklinikum Ulm AöR
Department Name
Institut für Transfusionsmedizin
Principal Investigator Name
Hubert Schrezenmeier
Principal Investigator Email
h.schrezenmeier@blutspende.de
Contact Person Name
Hubert Schrezenmeier
Contact Person Email
h.schrezenmeier@blutspende.de
Site Name
Universitaetsklinikum Essen AöR
Department Name
Klinik für Hämatologie und Stammzelltransplantation
Principal Investigator Name
Alexander Roeth
Principal Investigator Email
alexander.roeth@uk-essen.de
Contact Person Name
Alexander Roeth
Contact Person Email
alexander.roeth@uk-essen.de

Sponsor

Primary sponsor

Full Name
F. Hoffmann-La Roche AG
Organisation Type
Pharmaceutical company
Country Of Registered Address
Switzerland

Contract research organisations

Name
Parexel International Limited
Responsibilities
Randomization
Name
Icon Clinical Research Limited
Responsibilities
Patient Reported Outcomes
Name
IQVIA Limited
Responsibilities
FSP monitoring; Global CRO; patient reported outcomes functions (IQVIA Inc. and IQVIA Limited entries provide CRO services)
Name
Fortrea Inc.
Responsibilities
Mobile Clinical Services
Name
Icon Development Solutions LLC
Responsibilities
Analytical Laboratory / analytical support

Third parties

  • {"country":"Belgium","full_name":"Europese Organisatie Voor Onderzoek En Behandeling Van Kanker Organisation Europeenne Pour La Recherche Et Le Traitement Du Cancer European Organi","duties_or_roles":"Patient Reported Outcomes","organisation_type":"Patient organisation/association"}
  • {"country":"United States","full_name":"Fortrea Inc.","duties_or_roles":"Mobile Clinical Services","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"FACIT.Org Inc.","duties_or_roles":"Patient Reported Outcomes","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Parexel International Limited","duties_or_roles":"Randomization","organisation_type":"Pharmaceutical company"}
  • {"country":"Ireland","full_name":"Icon Clinical Research Limited","duties_or_roles":"Patient Reported Outcomes","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Iqvia Inc.","duties_or_roles":"Patient Reported Outcomes","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"IQVIA Limited","duties_or_roles":"FSP monitoring","organisation_type":"Pharmaceutical company"}
  • {"country":"Belgium","full_name":"MEDPACE LABORATORIES","duties_or_roles":"Analytical Laboratory","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United States","full_name":"Icon Development Solutions LLC","duties_or_roles":"Analytical Laboratory","organisation_type":"Pharmaceutical company"}
  • {"country":"Switzerland","full_name":"Labcorp Central Laboratory Services SARL","duties_or_roles":"Central lab","organisation_type":"Pharmaceutical company"}
  • {"country":"Japan","full_name":"Cmic Pharma Science Co. Ltd.","duties_or_roles":"Analytical Laboratory","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Publicis Healthcare Communications Group Limited","duties_or_roles":"Patient and site materials","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"IQVIA Limited","duties_or_roles":"Global CRO","organisation_type":"Pharmaceutical company"}
  • {"country":"United Kingdom","full_name":"Q Squared Solutions Limited","duties_or_roles":"Analytical Laboratory","organisation_type":"Non-Pharmaceutical company"}

Investigational products

Investigational Product Name
Crovalimab
Active Substance
CROVALIMAB
Modality
Monoclonal antibody
Routes Of Administration
INTRAVENOUS
Route
Intravenous
Authorisation Status
prodAuthStatus 1
Maximum Dose
1500 mg
Investigational Product Name
ECULIZUMAB
Active Substance
ECULIZUMAB
Modality
Monoclonal antibody
Routes Of Administration
INTRAVENOUS
Route
Intravenous
Authorisation Status
prodAuthStatus 2
Maximum Dose
900 mg

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