Clinical trial • Phase II • Oncology

3,4-DIMETHYL-N-(2-PHENYL-1H-PYRROLO[2,3-B]PYRIDIN-5-YL)-1H-PYRAZOLE-5-CARBOXAMIDE for Advanced systemic mastocytosis

Phase II trial of 3,4-DIMETHYL-N-(2-PHENYL-1H-PYRROLO[2,3-B]PYRIDIN-5-YL)-1H-PYRAZOLE-5-CARBOXAMIDE for Advanced systemic mastocytosis.

Overview

Trial Therapeutic Area
Oncology
Trial Disease
Advanced systemic mastocytosis
Trial Stage
Phase II
Drug Modality
Small molecule

Key dates

Initial CTIS Submission Date
30-04-2024
First CTIS Authorization Date
06-06-2024

Trial design

open-label, none/not specified-controlled, adaptive Phase II trial in Spain, Belgium, Poland and others.

Open Label
Yes
Comparator
None/Not specified
Adaptive
True, Part 1 is dose optimization (adaptive dose-finding) with dose modifications based on safety/PK/PD; Part 2 includes dose confirmation and an expansion stage—stage-based design with dose optimization/confirmation elements.
Single Multiple Or Escalation Dose Combined
Yes
Target Sample Size
80

Eligibility

Recruits 80 Vulnerable population selected. Subject information and informed consent forms (main ICFs and pregnant partner ICFs) and data processing consent forms are included in the provided documents in multiple country-specific versions (e.g., Spanish, Dutch, French, German, Italian, Polish, Norwegian, English). No specific assent process for minors is described in the available records..

Vulnerable Population
Vulnerable population selected. Subject information and informed consent forms (main ICFs and pregnant partner ICFs) and data processing consent forms are included in the provided documents in multiple country-specific versions (e.g., Spanish, Dutch, French, German, Italian, Polish, Norwegian, English). No specific assent process for minors is described in the available records.

Inclusion criteria

  • {"criterion_text":"- Diagnosed with 1 of the following advanced mastocytosis diagnoses: 1. Aggressive Systemic Mastocytosis (ASM) 2. Systemic Mastocytosis with an Associated Hematologic Neoplasm (SM-AHN) 3. Mast Cell Leukemia (MCL)\n- Measurable disease according to modified IWG-MRT-ECNM criteria\n- ECOG Status 0 to 3\n- Have clinically acceptable laboratory screening results (clinical chemistry, hematology) within certain limits\n- Other protocol-defined inclusion criteria apply."}

Exclusion criteria

  • {"criterion_text":"- Persistent toxicity from previous therapy for Advanced Systemic Mastocytosis that has not resolved to ≤ Grade 1\n- Received strong CYP3A4 inhibitors or inducers within 14 days or 5 drug half-lives, whichever is longer, before the first dose of study drug.\n- Need for treatment with high dose steroids\n- Associated hematologic neoplasm requiring immediate antineoplastic therapy\n- Clinically significant cardiac disease\n- Known positivity for the FIP1L1 PDGFRA fusion (patients with eosinophilia without detectable KIT D816V mutation must also lack the PDGFRA fusion mutation prior to enrolment)\n- Seropositive for human immunodeficiency virus (HIV) 1 or 2, positive for hepatitis B surface antigen, or positive for hepatitis C virus (HCV) antibody\n- History of clinically significant bleeding event within 30 days before the first dose of study drug or need for therapeutic anticoagulation on study\n- Diagnosed with or treated for malignancy other than the disease under study within the prior 3 years before enrollment\n- Received any cytoreductive therapy or any investigational agent less than 14 days, and for cladribine, interferon alpha, pegylated interferon, and any antibody therapy less than 28 days, before screening bone marrow biopsy\n- Received hematopoietic growth factor support within 14 days before the first dose of study drug."}

Endpoints

Primary endpoints

  • {"endpoint_text":"- Part 1: Dose Optimization - Safety assessments and dose modifications; - PK and pharmacodynamic assessments; - Overall response rate (ORR)","definition_or_measurement_approach":"Safety assessments and dose modifications (safety/tolerability assessments), pharmacokinetic (PK) and pharmacodynamic (PD) assessments, and Overall Response Rate (ORR) as the efficacy measure."}
  • {"endpoint_text":"- Part 2 Stage 1: Dose Confirmation - Safety assessments and dose modifications - PK and pharmacodynamic assessments - Overall response rate (ORR)","definition_or_measurement_approach":"Safety assessments and dose modification criteria, PK and PD assessments to confirm dose exposure, and Overall Response Rate (ORR) as efficacy endpoint."}
  • {"endpoint_text":"- Part 2 Stage 2: Expansion - Overall response rate (ORR)","definition_or_measurement_approach":"Overall Response Rate (ORR) measured in the expansion cohort at the selected optimal dose."}

Secondary endpoints

  • {"endpoint_text":"- Part 1 and Part 2: Incidence of AEs, SAEs, AEs leading to dose modifications, and changes from baseline in laboratory results","definition_or_measurement_approach":"Adverse events (AEs), serious adverse events (SAEs), AEs causing dose changes and laboratory value changes from baseline; standard AE/SAE reporting and laboratory monitoring."}
  • {"endpoint_text":"- Part 1 and Part 2: Duration Of Response (DOR), Time to Response (TTR), Progression Free Survival (PFS), Overall Survival (OS), Pure Pathologic Response (PPR)","definition_or_measurement_approach":"Standard oncology time-to-event measures: DOR, TTR, PFS, OS; Pure Pathologic Response (PPR) per protocol-defined criteria."}
  • {"endpoint_text":"- Part 1 and Part 2: Changes in the levels of serum tryptase","definition_or_measurement_approach":"Measured serum tryptase concentrations over time (central laboratory assays) to assess pharmacodynamic effect."}
  • {"endpoint_text":"- Part 1 and Part 2: Changes in the levels of KIT D816V mutation allele burden in blood and bone marrow","definition_or_measurement_approach":"Quantitative assessment of KIT D816V allele burden in blood and bone marrow samples (mutational analysis) to evaluate molecular response."}
  • {"endpoint_text":"- Part 1 and Part 2: Change in pathologic findings in the blood and bone marrow including mast cell infiltration, monocytosis, and eosinophilia","definition_or_measurement_approach":"Histopathologic evaluation of blood and bone marrow for mast cell infiltration, monocytosis, eosinophilia and other pathologic changes."}
  • {"endpoint_text":"- Part 1 and Part 2: Plasma concentrations of bezuclastinib","definition_or_measurement_approach":"Pharmacokinetic measurement of plasma concentrations of bezuclastinib."}
  • {"endpoint_text":"- Part 1 and Part 2: Change from baseline in PGIS, PGIC, MC-QoL and MAS","definition_or_measurement_approach":"Patient-reported outcomes: changes from baseline in PGIS, PGIC, MC-QoL and MAS instruments per protocol schedule."}

Recruitment

Planned Sample Size
80
Recruitment Window Months
66
Consent Approach
Informed consent is obtained using country-specific Subject Information and Informed Consent Forms (main ICFs) and associated documents; pregnant-partner ICFs and data processing consent forms are included. ICF documents are provided in multiple country/language versions (examples present for Spain, Belgium (Dutch/French/German), Italy, Poland, Austria, Norway, France, Netherlands, Germany, and English-language materials). The consent forms and supporting materials are the documented mechanism for obtaining consent; no specific assent process for minors is described in the available documents.

Geography

Total Number Of Sites
21
Total Number Of Participants
60

Spain

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
14-04-2025
Processing Time Days
332
Number Of Sites
3
Number Of Participants
7

Sites

Site Name
Hospital Universitari Vall D Hebron
Department Name
Hematology
Contact Person Name
Olga Salamero Garcia
Contact Person Email
osalamero@vhebron.net
Site Name
Institut Catala D'oncologia
Department Name
Hematology
Contact Person Name
Helena Pomares Marin
Contact Person Email
hpomares@iconcologia.net
Site Name
Hospital Universitario Ramon Y Cajal
Department Name
Hematology
Contact Person Name
Miguel Piris Villaespesa
Contact Person Email
miguel.piris@salud.madrid.org

Belgium

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
11-04-2025
Processing Time Days
329
Number Of Sites
1
Number Of Participants
7

Sites

Site Name
Centre hospitalier universitaire de Liege
Department Name
Oncology
Contact Person Name
Aurelie Jaspers
Contact Person Email
aurelie.jaspers@chuliege.be

Poland

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
15-04-2025
Processing Time Days
333
Number Of Sites
1
Number Of Participants
7

Sites

Site Name
Uniwersytecki Szpital Kliniczny Nr 1 W Lublinie
Department Name
Hematology
Contact Person Name
Marek Hus
Contact Person Email
marek.hus@umlub.pl

Austria

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
16-04-2025
Processing Time Days
334
Number Of Sites
1
Number Of Participants
6

Sites

Site Name
Medical University Of Vienna
Department Name
Department of Medicine I Clinical Division of Hematology and Hemostaseology
Contact Person Name
Wolfgang Sperr

Norway

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
14-04-2025
Processing Time Days
332
Number Of Sites
1
Number Of Participants
6

Sites

Site Name
Oslo University Hospital HF
Department Name
Hematology
Contact Person Name
Ingunn Dybedal
Contact Person Email
idybedal@ous-hf.no

France

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
16-04-2025
Processing Time Days
334
Number Of Sites
3
Number Of Participants
7

Sites

Site Name
Centre Hospitalier Universitaire De Toulouse
Department Name
Service de Dermatologie
Contact Person Name
Cristina Livideanu
Contact Person Email
livideanu.c@chu-toulouse.fr
Site Name
Assistance Publique Hopitaux De Paris
Department Name
Service Hematologie Adultes
Contact Person Name
Olivier Hermine
Contact Person Email
olivier.hermine@aphp.fr
Site Name
Centre Hospitalier Universitaire De Poitiers
Department Name
Dermatology and Oncology department
Contact Person Name
Ewa Wierzbicka- Hainaut
Contact Person Email
ewa.hainaut@chu-poitiers.fr

Italy

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
16-04-2025
Processing Time Days
334
Number Of Sites
6
Number Of Participants
6

Sites

Site Name
Fondazione IRCCS Policlinico San Matteo
Department Name
UOC Hematology I
Contact Person Name
Chiara Elena
Contact Person Email
c.elena@smatteo.pv.it
Site Name
Azienda Ospedaliero-Universitaria Di Bologna IRCCS Istituto Di Ricerca E Di Cura A Carattere Scientifico
Department Name
Hematology
Contact Person Name
Cristina Papayannidis
Contact Person Email
cristina.papayannidis@unibo.it
Site Name
Centro Ricerche Cliniche Di Verona S.r.l.
Department Name
Hematology
Contact Person Name
Massimiliano Bonifacio
Site Name
Careggi University Hospital
Department Name
Hematology
Contact Person Name
Francesco Mannelli
Contact Person Email
francesco.mannelli@unifi.it
Site Name
Azienda Ospedaliera Universitaria San Giovanni Di Dio E Ruggi d'Aragona
Department Name
Division of Allergy and Clinical Immunology
Contact Person Name
Massimo Triggiani
Contact Person Email
mtriggiani@unisa.it
Site Name
Universita' Degli Studi Di Roma La Sapienza
Department Name
Hematology
Contact Person Name
Massimo Breccia
Contact Person Email
breccia@bce.uniroma1.it

Netherlands

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
14-04-2025
Processing Time Days
332
Number Of Sites
1
Number Of Participants
7

Sites

Site Name
Universitair Medisch Centrum Groningen
Department Name
Hematology
Contact Person Name
Saskia Karina Klein
Contact Person Email
s.k.klein@umcg.nl

Germany

Earliest CTIS Part Ii Submission Date
17-05-2024
Latest Decision Or Authorization Date
16-04-2025
Processing Time Days
334
Number Of Sites
4
Number Of Participants
7

Sites

Site Name
Universitaetsklinikum Aachen AöR
Department Name
Klinik für Hämatologie, Onkologie, Hämostaseologie und Stammzelltransplantation (Med. Klinik IV)
Contact Person Name
Jens Panse
Contact Person Email
jpanse@ukaachen.de
Site Name
Universitaetsklinikum Mannheim GmbH
Department Name
III. Medizinische Klinik, Universität heidelberg Medizinische Fakultät Mannheim
Contact Person Name
Juliana Schwaab
Site Name
Universitaetsklinikum Schleswig-Holstein AöR
Department Name
Hematology and Oncology
Contact Person Name
Nikolas von Bubnoff
Contact Person Email
Nikolas.vonBubnoff@uksh.de
Site Name
Medical Center - University Of Freiburg
Department Name
Dept. of Medicine, Hematology, Oncology and Stem Cell Transplantation
Contact Person Name
Khalid Shoumariyeh

Sponsor

Primary sponsor

Full Name
Cogent Biosciences Inc.
Organisation Type
Pharmaceutical company
Country Of Registered Address
United States

Contract research organisations

Name
Icon Clinical Research Limited
Name
Ppd Inc.
Responsibilities
Bioanalytics
Name
Icon Laboratory Services Inc.
Responsibilities
Laboratory - Shipment and Storage of Clinical Samples
Name
Advanced Clinical GmbH

Third parties

  • {"country":"United States","full_name":"Verasafe LLC","duties_or_roles":"Data Protection Officer and Data Protection Representative services","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United States","full_name":"Icon Laboratory Services Inc.","duties_or_roles":"Laboratory - Shipment and Storage of Clinical Samples","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"Germany","full_name":"Advanced Clinical GmbH","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Eresearchtechnology Inc.","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Eclinical Solutions LLC","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Njs Associates Company","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Arup Laboratories Inc.","duties_or_roles":"Laboratory -Serum Tryptase (centrally) and mutational analysis","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United States","full_name":"Signant Health Global LLC","duties_or_roles":"QoL licensing, translations, and system","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Suvoda LLC","duties_or_roles":"IVRS","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United States","full_name":"Gene By Gene Ltd.","duties_or_roles":"hereditary alpha tryptasemia (HAT) testing","organisation_type":"Laboratory/Research/Testing facility"}
  • {"country":"United States","full_name":"Block Clinical Inc.","duties_or_roles":"Patient Concierge Service. Travel and Reimbursement Services","organisation_type":"Non-Pharmaceutical company"}
  • {"country":"United States","full_name":"Ppd Inc.","duties_or_roles":"Bioanalytics","organisation_type":"Pharmaceutical company"}
  • {"country":"Ireland","full_name":"Icon Clinical Research Limited","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"Switzerland","full_name":"United BioSource (Suisse) S.A.","duties_or_roles":"","organisation_type":"Pharmaceutical company"}
  • {"country":"United States","full_name":"Bioclinica Inc.","duties_or_roles":"Medical image analysis/ review - X-ray, MRI, ultrasound, etc","organisation_type":"Laboratory/Research/Testing facility"}

Investigational products

Investigational Product Name
CGT9486
Active Substance
3,4-DIMETHYL-N-(2-PHENYL-1H-PYRROLO[2,3-B]PYRIDIN-5-YL)-1H-PYRAZOLE-5-CARBOXAMIDE
Modality
Small molecule
Routes Of Administration
ORAL
Route
ORAL
Maximum Dose
300 mg
Investigational Product Name
CGT9486
Active Substance
3,4-DIMETHYL-N-(2-PHENYL-1H-PYRROLO[2,3-B]PYRIDIN-5-YL)-1H-PYRAZOLE-5-CARBOXAMIDE
Modality
Small molecule
Routes Of Administration
ORAL
Route
ORAL
Maximum Dose
400 mg

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